Communicating bronchopulmonary foregut malformation (CBPFM) is a congenital pulmonary malformation characterized by isolated pulmonary tissue connecting with the digestive tract. To date, there have been few reports on observations associated… Click to show full abstract
Communicating bronchopulmonary foregut malformation (CBPFM) is a congenital pulmonary malformation characterized by isolated pulmonary tissue connecting with the digestive tract. To date, there have been few reports on observations associated with CBPFM in utero. Herein, we describe the case of a male infant who was monitored via fetal ultrasound and magnetic resonance imaging (MRI) during the fetal period due to mesocardia and horseshoe kidney and was found to have CBPFM after birth. Although the volumes of both lungs were maintained in utero, that of the affected lung decreased rapidly soon after birth. Despite this dynamic change, the patient did not develop severe respiratory failure until 5 months old. This is the first report of a patient with CBPFM who exhibited an unusual perinatal course. Written informed consent for the publication was obtained from the patient’s parents.
               
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