LAUSR

Leiomyosarcoma is a malignant tumor arising from smooth muscle cells in the alimentary tract, retroperitoneum, genitourinary system, or soft tissue. Primary leiomyosarcoma of vascular origin is a rare tumor and comprises less than 2% of all leiomyosarcomas [1]. The inferior vena cava is the most commonly affected vessel followed by the large central veins and then the long saphenous vein [1, 2]. Leiomyosarcomas arising from the ovarian veins are extremely rare. Only a few sporadic cases have been described in previous studies with the development of hepatic metastasis in one case report [2–6]. To the best of our knowledge, this is the first case report in English literature of a retroperitoneal leiomyosarcoma arising from the ovarian vein with interval development of skeletal and adrenal metastases. The radiological images, as well as pathological findings, are illustrated.