LAUSR

Gastrointestinal stromal tumor (GIST) which occurs outside of alimentary canal without any connection is called as extra gastrointestinal stromal tumor (EGIST). Primary retroperitoneal EGISTs are extremely uncommon with insufficient awareness for rare prevalence. In addition, so-called adrenal EGISTs were reported by few authors. Here we reported a rare and interesting case about primary retroperitoneal extra gastrointestinal stromal in the left adrenal region. The tumor was diagnosed as pheochromocytoma preoperatively due to symptoms, abnormal hormone levels and imaging features. Tumor resection was operated after preoperative preparation for pheochromocytoma. However, postoperative pathology verified as primary retroperitoneal EGIST without relation to the left adrenal region or digestive tract.