LAUSR

Primary cardiac neoplasms are extremely rare, with an incidence at autopsy of 0.0001% to 0.03%. Most (75%) primary cardiac tumors are benign. The majority of malignant cardiac tumors are sarcomas, of which 30% are angiosarcomas. Other subtypes include rhabdomyosarcoma, malignant fibrous histiocytoma, and fibrosarcoma. Despite being the most common malignant cardiac tumor, cardiac angiosarcoma is often overlooked because of its rarity and nonspecific presentation. As a result of its aggressive nature and late diagnosis, the prognosis remains poor. We describe a case of tumor in the right ventricular outflow tract (RVOT) and main pulmonary artery (MPA) that eluded preoperative diagnosis despite multimodality imaging.