LAUSR

Electroanatomical mapping in these individuals has an important value because of the anatomical distortion. Introduction Ebstein anomaly (EA) is a congenital heart defect characterized by the apical displacement and insertion of the septal and posterior tricuspid leaflets inside the right ventricle, which may cause different degrees of tricuspid regurgitation. The anterior leaflet usually is elongated, tethered, and fenestrated, but mobile. This tricuspid malformation is associated with right atrium and ventricle changes resulting in important electrophysiological modifications, such as prolonged intraatrial activation, right bundle branch block, and occurrence of multiple accessory pathways. The symptoms may appear at any age, from intrauterine life until adulthood. Early presentation of EA occurs when there is severe tricuspid regurgitation, in particular when associated with other anomalies, such as anatomical or functional right ventricular (RV) outflow tract obstruction. Arrhythmia is a common manifestation in adulthood. The purpose of this case report is to describe an unusual presentation of wide QRS tachycardia in a patient with EA.