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Highlights • Lymphangioleiomyomatosis (LAM) is a rare and fatal disease.• Its specific treatment is still unclear.• The presentation of abdominal LAM without pulmonary findings is unusual.• We report an Extrapulmonary… Click to show full abstract
Highlights • Lymphangioleiomyomatosis (LAM) is a rare and fatal disease.• Its specific treatment is still unclear.• The presentation of abdominal LAM without pulmonary findings is unusual.• We report an Extrapulmonary -LAM treated with abdominal and thoracic surgery, radiotherapy and finally sirolimus.• The follow-up period was complicated, as no specific center or national institution was available for these patients.
Keywords:
lymphangioleiomyomatosis;
case;
report extrapulmonary;
report;
extrapulmonary manifestation;
manifestation lymphangioleiomyomatosis
Journal Title: International Journal of Surgery Case Reports
Year Published: 2017
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Journal Title: International Journal of Surgery Case Reports
Year Published: 2017
Link to full text (if available)
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recommendations!