LAUSR

AAV: antineutrophil cytoplasmic antibodyeassociated vasculitis ACR: American College of Rheumatology ANA: antinuclear antibody ANCA: antineutrophil cytoplasmic antibody anti-MPO: antimyeloperoxidase MCTD: mixed connective tissue disease p-ANCA: perinuclear antineutrophil cytoplasmic antibody RNP: ribonucleoprotein SLE/AAV: systemic lupus erythematosus antineutrophil cytoplasmic antibodyeassociated vasculitis overlap syndrome INTRODUCTION Systemic lupus erythematosus and antineutrophil cytoplasmic antibody (ANCA)eassociated vasculitis (SLE/AAV) overlap syndrome is a rare disease originally described in 2008. With only a few reports in the literature, this condition is characterized by aggressive crescentic glomerulonephritis, arthritis, cutaneous involvement, and both antinuclear antibody (ANA) and ANCA. Dermatologic manifestations are common and may occur at initial presentation. Although skin lesions may vary in morphology, the most commonly reported include cutaneous nodules and ecchymoses. Few reports have characterized the cutaneous findings seen in this disorder. We report a young woman with SLE/ AAV overlap syndrome who presented with a macular eruption and histopathology findings demonstrating interface dermatitis.