A 14-year-old otherwise healthy boy presented with rightsided small eye with leukocoria since the age of four. At that time, his parents neglected these signs until the leukocoria bothered the… Click to show full abstract
A 14-year-old otherwise healthy boy presented with rightsided small eye with leukocoria since the age of four. At that time, his parents neglected these signs until the leukocoria bothered the patient who asked for treatment. His visual acuity was reduced to hand motion on the right eye. External examination revealed a right esotropia with leukocoria. Slit-lamp examination of the right eye revealed small corneal diameters and a shallow anterior chamber (Fig. 1A). Furthermore, we noted a posterior synechia (Fig. 1A, white arrow), elongated and stretched ciliary processes (Fig. 1A, white star) with a white and partially resorbed cataract preventing funduscopy. The left eye was normal. Ocular B-scan and Doppler ultrasonography of the right eye showed a short axial length (19.7 mm, normal > 21 mm), a cataractous lens and an echogenic dense
               
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