LAUSR

Rationale: Harlequin syndrome is an extremely rare benign condition characterized by unilateral facial flushing and sweating. Patient concern: An 11-year-old boy presented with complaint of a right neck mass of 1-month duration. Diagnosis: The preoperative diagnosis was neurogenic tumor of vagus nerve or sympathetic nerve. Interventions: We performed right neck mass removal under general anesthesia. Outcomes: We report a case of harlequin syndrome associated with Horner syndrome in an 11-year boy who underwent excision of right neck schwannoma. Lessons: Clinicians should consider the point that harlequin syndrome could occur as a first sign of more serious conditions.