LAUSR

Klippel-Tre´naunay syndrome (KTS) is a rare congenital mesodermal alteration characterized by the clinical triad of varicose veins, hypertrophy of the soft tissues and bones, and cutaneous haemangiomas. Although uncommon, gastrointestinal (GI) hemorrhage is a potentially serious complication secondary to diffuse hemangiomatous involvement of the gut. Diffuse cavernous haemangiomas of the distal colon and rectum are the commonest reported causes of GI bleeding in KTS [1]. Management options vary from conservative approaches to resection of the affected bowel segment depending on the extent and the severity of blood loss [1]. Rectal haemangiomatosis has usually been treated by open abdominoperineal resection or sphincter-saving procedures with coloanal anastomosis [1] [2].