LAUSR

Alterations in oestrogen metabolism: implications for higher penetrance of familial pulmonary arterial hypertension in females. Eur Respir J 2009;34:1093–1099. 8. Simonneau G, Montani D, Celermajer DS, Denton CP, Gatzoulis MA, Krowka M, et al. Haemodynamic definitions and updated clinical classification of pulmonary hypertension. Eur Respir J 2019;53:1801913. 9. Jutant E-M, Girerd B, Jaı̈s X, Savale L, O’Connell C, Perros F, et al. Pulmonary hypertension associated with neurofibromatosis type 1. Eur Respir Rev 2018;27:180053. 10. Montani D, Price LC, Dorfmuller P, Achouh L, Jaı̈s X, Yaı̈ci A, et al. Pulmonary veno-occlusive disease. Eur Respir J 2009;33:189–200. 11. Humbert M, Maı̂tre S, Capron F, Rain B, Musset D, Simonneau G. Pulmonary edema complicating continuous intravenous prostacyclin in pulmonary capillary hemangiomatosis. Am J Respir Crit Care Med 1998;157:1681–1685. 12. Farber HW, Miller DP, Poms AD, Badesch DB, Frost AE, Muros-Le Rouzic E, et al. Five-year outcomes of patients enrolled in the REVEAL registry. Chest 2015;148:1043–1054. 13. Tibbles JA, Cohen MM Jr. The proteus syndrome: the elephant man diagnosed. Br Med J (Clin Res Ed) 1986;293:683–685.