LAUSR

Backgroud: Idiopathic pulmonary fibrosis and idiopathic non-specific interstitial pneumonia are categorized as idiopathic chronic fibrosing interstitial pneumonia (FIP). Survival after respiratory hospitalization (RH) in FIP as a whole has not been sufficiently examined. Methods: Three hundred and ninety-four consecutive patients with FIP (73.1±7.9 y.o.) who underwent evaluation as general practice in our University hospital between January 2008 and August 2017 and were followed-up thereafter were included in the study. The diagnosis of FIP was made according to the ATS/ERS statement 2013. The occurrence of RH and the survival after the RH were reviewed. Results: The mean follow-up period was 1130±935 days, and 127 patients (32.2%) were deceased. Multivariate regression analysis showed that female sex (HR 0.30, 95%CI 0.18-0.51, p Conclusions: Survival after RH with AE and non-AE were equivalent in FIP. Survival after RH in patients with definite UIP pattern on chest HRCT was worse than those with non-definite UIP pattern.