LAUSR

With increasing diagnostic and therapeutic modalities, more and more patients with congenital heart disease (CHD) survive till adulthood and may present for coincident elective or emergent noncardiac surgery.[1] Such patients, especially with unrepaired or unpalliated cardiac defects, offer a great challenge because of their complex physiological modifications secondary to chronic hypoxia and excessive or reduced pulmonary blood flow. Double outlet right ventricle (DORV) is a complex cardiac defect that comes under the broad category of single ventricle physiology. We present the successful management of a patient with DORV for emergent noncardiac surgery.