LAUSR

An 88-year-old woman with progressive dementia and parkinsonism unresponsive to L-dopa was referred to the emergency department for traumatic brain injury. Skull X-rays [Figure 1] and brain CT [Figure 2] showed extensive and symmetrical intracranial calcification located in dentate nuclei, occipital cortex, thalami, basal ganglia, and centrum semiovale. Routine blood tests and parathormone were normal. Neurological examination showed akinetic-rigid parkinsonism and severe cognitive impairment. Despite a negative family history, patient’s features were suggestive of Fahr’s syndrome. Fahr’s syndrome, or idiopathic basal ganglia calcification (IBGC), is a rare neurological disorder characterized by abnormal deposition of calcium in brain.