LAUSR

999 Primary angiitis of the central nervous system (PACNS) represents a rare but important severe inflammatory vasculitis of brain, meninges, and/or spinal cord in the absence of any systemic vasculitis elsewhere.[1] Historical records dates back to early 20th century when Harbitz described an unknown form of angiitis affecting the central nervous system (CNS).[2] It was first proposed to be a distinct clinicopathological entity in 1959 by Cravioto and Feign who named it ‘non‐infectious granulomatous angiitis of CNS’.[3]