Multimodality imaging of Abernethy malformation
Sign Up to like & getrecommendations! Published in 2022 at "Echocardiography"
DOI: 10.1111/echo.15324
Abstract: Abernethy malformation, or congenital extrahepatic portosystemic venous shunt, is a rare anomaly involving the portal venous system. Despite its rarity, it is increasingly being reported, and therefore, it is important to diagnose given the potential… read more here.
Keywords: malformation; imaging abernethy; abernethy malformation; multimodality imaging ... See more keywords
Abernethy malformation associated with Caroli’s syndrome in a patient with a PKHD1 mutation: a case report
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DOI: 10.1186/s13000-017-0647-y
Abstract: BackgroundAbernethy malformation is a rare congenital anomaly characterised by the partial or complete absence of the portal vein and the subsequent development of an extrahepatic portosystemic shunt. Caroli’s disease is a rare congenital condition characterised… read more here.
Keywords: caroli syndrome; case; malformation; abernethy malformation ... See more keywords
Treatment Option for Abernethy Malformation—Two Cases Report and Review of the Literature
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DOI: 10.3389/fped.2020.497447
Abstract: Background: Abernethy malformation is a rare vascular anomaly of the portal venous system, which is also known as congenital portosystemic shunts (CPSS). The clinical manifestations of this anomaly can be serious, including hepatopulmonary syndrome(HPS), which… read more here.
Keywords: cyanosis; treatment; case; malformation ... See more keywords
Novel transcatheter treatment for staged closure of Abernethy malformation with portal hypoplasia
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DOI: 10.4103/apc.apc_189_20
Abstract: Portosystemic shunts are rare congenital malformations that come to attention due to various hepatic and extrahepatic manifestations. Management of this malformation is dictated by the presence and adequacy of intrahepatic portal radicals. Staged occlusion of… read more here.
Keywords: abernethy malformation; malformation; transcatheter treatment; novel transcatheter ... See more keywords
Type II Abernethy Malformation in a Patient with Primary Budd-Chiari Syndrome.
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DOI: 10.5604/01.3001.0012.7933
Abstract: Budd-Chiari syndrome (BCS) is a heterogeneous group of disorders characterized by hepatic venous outflow obstruction. Abernethy malformation is a congenital vascular malformation defined by diversion of portal blood away from the liver. Both conditions are… read more here.
Keywords: budd chiari; chiari syndrome; malformation; type abernethy ... See more keywords