Successful treatment of acquired von Willebrand syndrome associated with monoclonal gammopathy
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DOI: 10.1007/s00508-022-02012-3
Abstract: Acquired von Willebrand syndrome is exceedingly rare and accounts for only 1–3% of von Willebrand disease cases. In this short report, we present our own cases of acquired von Willebrand syndrome associated with monoclonal gammopathy.… read more here.
Keywords: acquired von; monoclonal gammopathy; willebrand syndrome; von willebrand ... See more keywords
Factors related to the development of acquired von Willebrand syndrome in patients with essential thrombocythemia and polycythemia vera.
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DOI: 10.1016/j.ejim.2016.11.011
Abstract: OBJECTIVE We characterized acquired von Willebrand syndrome (AVWS) among essential thrombocythemia (ET) and polycythemia vera (PV) patients. METHODS A review of patients with ET or PV evaluated for AVWS. RESULTS Of 116 patients with ET,… read more here.
Keywords: jak2 v617f; among patients; von willebrand; platelet ... See more keywords
Samuel Armstrong Lane's first successful treatment of haemophilia with blood transfusion in 1840: Could this also be the first successful bypassing therapy?
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DOI: 10.1111/hae.13645
Abstract: 1. Simone JV, Cornet JA, Abildgaard CF. Acquired von Willebrand’s syn‐ drome in systemic lupus erythematosus. Blood. 1968;31(6):806‐812. 2. Federici AB, RandJH, et al. Acquired von Willebrand syn‐ drome: data from an international registry. Thromb… read more here.
Keywords: willebrand syndrome; willebrand; blood; von willebrand ... See more keywords
Acquired von Willebrand syndrome and lymphoid neoplasms: A review of malignancy management, and propositions of practical recommendations
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DOI: 10.1111/hae.14648
Abstract: Acquired von Willebrand syndrome (AWS) is a rare and potentially life‐threatening bleeding disorder. AWS is primarily associated with lymphocyte‐related disorders (AWS‐LRD), such as lymphoma and IgM monoclonal gammopathy of undetermined significance (MGUS), and plasmocyte‐related disorders… read more here.
Keywords: willebrand syndrome; von willebrand; acquired von; syndrome lymphoid ... See more keywords
Good syndrome: immunodeficiency associated with thymoma
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DOI: 10.1111/imj.13950
Abstract: acquired von Willebrand syndrome: a retrospective single-centre cohort study. J Thromb Haemost 2008; 6: 569–76. 7 Vincentelli A, Susen S, Le Tourneau T, Six I, Fabre O, Juthier F et al. Acquired von Willebrand syndrome… read more here.
Keywords: willebrand syndrome; good syndrome; von willebrand; syndrome ... See more keywords
Contact activation and acquired von Willebrand syndrome during neonatal extracorporeal circulation
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DOI: 10.1111/jth.15058
Abstract: with APS and triple positivity are also positive in aPS/PT (tetra-positive aPL)7 and that aPS/PT more than aβ2GPI is responsible for LA activity in these patients.8 Finally, if aCL and aβ2GPI antibodies are of immunoglobulin… read more here.
Keywords: willebrand syndrome; syndrome neonatal; activation acquired; von willebrand ... See more keywords
ADAMTS13 inhibition to treat acquired von Willebrand syndrome during mechanical circulatory support device implantation
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DOI: 10.1111/jth.15889
Abstract: Acquired von Willebrand syndrome (aVWS) is common in patients with mechanical circulatory support (MCS) devices. In these patients, the high shear stress in the device leads to increased shear‐induced proteolysis of von Willebrand factor (VWF)… read more here.
Keywords: willebrand; mechanical circulatory; circulatory support; willebrand syndrome ... See more keywords
Perioperative diagnosis and impact of acquired von Willebrand syndrome in infants with congenital heart disease.
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DOI: 10.1182/blood.2022015699
Abstract: AVWS (acquired von Willebrand syndrome) has been reported in patients with congenital heart diseases (CHD) associated with shear stress caused by significant blood flow gradients. Its etiology and impact on intraoperative bleeding during pediatric cardiac… read more here.
Keywords: congenital heart; willebrand syndrome; von willebrand; vwf ratio ... See more keywords
Acquired Von Willebrand Disease in Patients with Waldenström Macroglobulinemia
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DOI: 10.1182/blood.v130.suppl_1.1088.1088
Abstract: Introduction: Acquired von Willebrand disease (VWD) is uncommonly observed in patients with Waldenstrom Macroglobulinemia (WM), and necessitates treatment intervention. The clinical characteristics for WM patients with acquired VWD, as well as outcomes following therapy have… read more here.
Keywords: acquired von; vwd; von willebrand; research funding ... See more keywords
[Relapse of acquired von Willebrand syndrome in a patient non-compliant with Crohn's disease].
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DOI: 10.1684/abc.2021.1692
Abstract: We report a case of acquired von Willebrand syndrome relapse in association with Crohn's disease, in a context of non-compliance in a 85-year-old woman suffering from epistaxis and melena. The acquired von Willebrand syndrome is… read more here.
Keywords: willebrand syndrome; acquired von; crohn disease; von willebrand ... See more keywords
Acquired von Willebrand Syndrome in a Patient with Multiple Comorbidities, Including MALT Lymphoma with IgA Monoclonal Gammopathy and Hyperviscosity Syndrome
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DOI: 10.2169/internalmedicine.9815-22
Abstract: Acquired von Willebrand syndrome (aVWS) develops with various underlying diseases. We herein report an individual with aVWS associated with mucosa-associated lymphoid tissue lymphoma in the lungs complicated by hyperviscosity syndrome, Sjögren's syndrome, and hypothyroidism. This… read more here.
Keywords: lymphoma; syndrome; hyperviscosity; von willebrand ... See more keywords