Leukocyte adhesion defect‐I: rare primary immune deficiency
Sign Up to like & getrecommendations! Published in 2017 at "Special Care in Dentistry"
DOI: 10.1111/scd.12249
Abstract: Leukocyte adhesion defect I is a rare disorder (1:1,000,000) caused by diminished expression of CD-18 β2 integrins on leukocytes leading to abnormal adhesion, migration, and chemotaxis. Clinical manifestations include delayed separation of umbilical cord, omphalitis,… read more here.
Keywords: defect rare; adhesion; leukocyte adhesion; adhesion defect ... See more keywords
Leucocyte adhesion defect presenting as fulminant sepsis in a new born
Sign Up to like & getrecommendations! Published in 2019 at "BMJ Case Reports"
DOI: 10.1136/bcr-2018-227065
Abstract: We present a term neonate with severe sepsis, presenting on day 10 of life. The neonate presented with bilateral purulent eye discharge and hepatosplenomegaly. On investigation, persistent leucocytosis was observed and thus the possibility of… read more here.
Keywords: leucocyte adhesion; adhesion defect; defect presenting; sepsis ... See more keywords