Spontaneous rupture of large bilateral renal angiomyolipomas in a patient with tuberous sclerosis complex: A case report and literature review
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DOI: 10.1016/j.eucr.2020.101124
Abstract: Enormous bilateral renal angiomyolipoma (AML) are extremely rare, their spontaneous bleeding also called Wunderlich's syndrom (WS) is also an unusual situation. It is considered as a life threatening condition requiring fast and effective care. We… read more here.
Keywords: patient tuberous; bilateral renal; case; angiomyolipomas ... See more keywords
The effect of sirolimus on angiomyolipoma is determined by decrease of fat-poor compartments and includes striking reduction of vascular structures
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DOI: 10.1038/s41598-021-87930-4
Abstract: Renal angiomyolipomas hemorrhage is associated with their size and vascular constitution. The effects of sirolimus on different components of angiomyolipomas was analyzed in patients with tuberous sclerosis complex, sporadic lymphangioleiomyomatosis and multiple sporadic angiomyolipomas. Thirty… read more here.
Keywords: reduction; fat poor; fat; effect ... See more keywords
Renal Manifestations of Tuberous Sclerosis Complex: Key Findings From the Final Analysis of the TOSCA Study Focussing Mainly on Renal Angiomyolipomas
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DOI: 10.3389/fneur.2020.00972
Abstract: Renal angiomyolipomas are one of the most common renal manifestations in patients with tuberous sclerosis complex (TSC), with potentially life-threatening complications and a poor prognosis. Despite the considerable progress in understanding TSC-associated renal angiomyolipomas, there… read more here.
Keywords: intervention; tuberous sclerosis; age; renal angiomyolipomas ... See more keywords