Echocardiographic characteristics of patients with antisynthetase syndrome
Sign Up to like & getrecommendations! Published in 2022 at "Pulmonary Circulation"
DOI: 10.1002/pul2.12084
Abstract: Abstract Right ventricular (RV) dysfunction and pulmonary hypertension (PH) occurs in approximately one‐third of patients with interstitial lung disease (ILD) and is associated with reduced 6‐minute walk distance (6MWD), and increased hospitalizations and mortality. Although… read more here.
Keywords: antisynthetase syndrome; dysfunction; echocardiographic characteristics; patients antisynthetase ... See more keywords
Nailfold videocapillaroscopy alterations in dermatomyositis, antisynthetase syndrome, overlap myositis, and immune-mediated necrotizing myopathy
Sign Up to like & getrecommendations! Published in 2019 at "Clinical Rheumatology"
DOI: 10.1007/s10067-019-04710-2
Abstract: The aim of our study was to investigate possible differences in nailfold videocapillaroscopy (NVC) features between patients with dermatomyositis (DM), overlap myositis (OM), antisynthetase syndrome (ASS), and immune-mediated necrotizing myopathy (IMNM). We performed a cross-sectional… read more here.
Keywords: nailfold videocapillaroscopy; ass; immune mediated; antisynthetase syndrome ... See more keywords
Antineutrophil cytoplasmic antibody positivity and cutaneous IgA vasculitis in a patient with antisynthetase syndrome
Sign Up to like & getrecommendations! Published in 2021 at "JAAD Case Reports"
DOI: 10.1016/j.jdcr.2021.10.012
Abstract: AAV: ANCA-associated vasculitis ANCA: antineutrophil cytoplasmic antibodies ASS: antisynthetase syndrome LCV: leukocytoclastic vasculitis INTRODUCTION Vasculitis is a disease process that results from inflammation of blood vessel walls. The clinical presentation is variable and dependent upon… read more here.
Keywords: vasculitis; antineutrophil cytoplasmic; cytoplasmic antibody; iga vasculitis ... See more keywords
Thigh MRI in antisynthetase syndrome, and comparisons with dermatomyositis and immune-mediated necrotising myopathy.
Sign Up to like & getrecommendations! Published in 2022 at "Rheumatology"
DOI: 10.1093/rheumatology/keac269
Abstract: OBJECTIVES To evaluate MRI changes to define muscle-lesion specific patterns in patients with antisynthetase syndrome (ASS), and compare them with those in other common idiopathic inflammatory myopathy (IIM) subtypes. METHODS Qualitative and semi-quantitative thigh MRI… read more here.
Keywords: antisynthetase syndrome; oedema; mri; dermatomyositis immune ... See more keywords
Antisynthetase syndrome pathogenesis: knowledge and uncertainties
Sign Up to like & getrecommendations! Published in 2018 at "Current Opinion in Rheumatology"
DOI: 10.1097/bor.0000000000000555
Abstract: Purpose of review Antisynthetase syndrome (ASyS) is an acquired myopathy characterized by the presence of myositis-specific autoantibodies directed against tRNA-synthetases. ASyS is potentially life threatening due to lung involvement and treatment remains a challenge to… read more here.
Keywords: asys pathogenesis; pathogenesis knowledge; pathogenesis; antisynthetase syndrome ... See more keywords
Muscle pathology of antisynthetase syndrome according to antibody subtypes
Sign Up to like & getrecommendations! Published in 2022 at "Brain pathology"
DOI: 10.1101/2022.04.25.22274260
Abstract: Antisynthetase syndrome is recently recognized as one of the major entities of autoimmune myositis. The prototype of antisynthetase syndrome is anti-Jo-1 antibody associated syndrome while the syndromes associated with non-Jo-1 antisynthetase antibodies are clinically and… read more here.
Keywords: pathology; antisynthetase syndrome; muscle; expression ... See more keywords
A prognostic analysis of antisynthetase syndrome‐related interstitial lung disease
Sign Up to like & getrecommendations! Published in 2022 at "International Journal of Rheumatic Diseases"
DOI: 10.1111/1756-185x.14428
Abstract: To analyze prognostic factors of antisynthetase syndrome (ASS)‐related interstitial lung disease (ILD). read more here.
Keywords: related interstitial; antisynthetase syndrome; lung disease; interstitial lung ... See more keywords
Subcutaneous immunoglobulins for the treatment of a patient with antisynthetase syndrome and secondary chronic immunodeficiency after anti-CD20 treatment: a case report
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Medical Case Reports"
DOI: 10.1186/s13256-017-1211-9
Abstract: BackgroundAntisynthetase syndrome is a rare and debilitating multiorgan disease characterized by inflammatory myopathy, interstitial lung disease, cutaneous involvement, and frequent chronic inflammation of the joints. Standard treatments include corticosteroids and immunosuppressants. In some cases, treatment… read more here.
Keywords: administration; treatment; case; antisynthetase syndrome ... See more keywords
Clinical features, prognostic factors, and survival of patients with antisynthetase syndrome and interstitial lung disease
Sign Up to like & getrecommendations! Published in 2022 at "Frontiers in Immunology"
DOI: 10.3389/fimmu.2022.872615
Abstract: Objective This study aimed to analyze the clinical features and prognostic factors of imaging progression and survival in patients with antisynthetase syndrome (ASS) complicated by interstitial lung disease (ILD) in a large Chinese cohort. Methods… read more here.
Keywords: antisynthetase syndrome; prognostic factors; features prognostic; clinical features ... See more keywords
A Proof-of-Concept Analysis of Plasma-Derived Exosomal microRNAs in Interstitial Pulmonary Fibrosis Secondary to Antisynthetase Syndrome
Sign Up to like & getrecommendations! Published in 2022 at "International Journal of Molecular Sciences"
DOI: 10.3390/ijms232314579
Abstract: Antisynthetase syndrome (ASSD) is an autoimmune disease characterized by the positivity of autoantibodies against different aminoacyl transfer RNA (tRNA) synthetases. Morbidity and mortality of this disease are highly affected by interstitial lung disease (ILD) which… read more here.
Keywords: antisynthetase syndrome; assd ild; pulmonary fibrosis; plasma derived ... See more keywords
The clinical manifestations at the onset of antisynthetase syndrome: A chameleon with multiple faces.
Sign Up to like & getrecommendations! Published in 2020 at "Reumatismo"
DOI: 10.4081/reumatismo.2020.1275
Abstract: The antisynthetase syndrome (ASS) is clinically characterized by fever, myositis, interstitial lung disease, joint involvement, mechanic's hands, or Raynaud's phenomenon, and the presence of antisynthetase autoantibodies. These clinical manifestations may not occur simultaneously. Therefore, the… read more here.
Keywords: mechanic hands; ass; clinical manifestations; raynaud phenomenon ... See more keywords