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Published in 2025 at "World Journal of Clinical Cases"
DOI: 10.12998/wjcc.v13.i33.113167
Abstract: Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous intermediate-grade soft tissue tumor characterized by COL1A1::PDGFB fusion in most cases. This fusion drives tumorigenesis and forms the basis for imatinib treatment, which acts by blocking platelet-derived growth…
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Keywords:
pdgfb rare;
beyond col1a1;
rare fusions;
dermatofibrosarcoma protuberans ... See more keywords