Budd‐chiari syndrome and acute liver failure: A complex condition requiring a rapid response
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DOI: 10.1002/lt.24695
Abstract: Thrombotic occlusion of all the hepatic veins is commonly referred to as Budd-Chiari syndrome (BCS). It presents as a manifestation of a systemic procoagulant condition which may be covert but is characterizable in most cases… read more here.
Keywords: liver failure; budd chiari; condition; chiari syndrome ... See more keywords
Ultrasonography in pediatric Budd–Chiari syndrome
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DOI: 10.1007/s00247-020-04753-7
Abstract: Budd–Chiari syndrome is a vascular pathology of the liver, commonly seen in adults and uncommon in children. Most children with Budd–Chiari syndrome present with ascites, and an etiology is found in only about 50%. Ultrasonography… read more here.
Keywords: budd chiari; pediatric budd; chiari syndrome;
Clinical Chiari syndrome or anatomical Chiari malformation? A conundrum revisited
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DOI: 10.1007/s00701-019-04175-x
Abstract: Despite about one hundred years of academic work, the general use of the term Chiari malformation remains unclear and continues to cause disagreement, if not confusion, among experts [1]. The term has been employed variably… read more here.
Keywords: symptomatology; chiari syndrome; selection; chiari ... See more keywords
Budd–Chiari syndrome has different presentations and disease severity during adolescence
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DOI: 10.1007/s12072-018-9880-z
Abstract: There are limited data on clinical profile of adolescent patients with Budd–Chiari syndrome (BCS). We studied clinical, radiological, thrombophilia profile and treatment outcomes in adolescent patients with BCS.MethodsForty-three consecutive patients of BCS with onset of… read more here.
Keywords: patients bcs; budd chiari; adolescence; chiari syndrome ... See more keywords
Pediatric Budd-Chiari Syndrome: A Case Series
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DOI: 10.1007/s13312-018-1397-y
Abstract: ObjectiveTo study the diagnostic methods and treatment outcomes in children with Budd-Chiari syndrome.MethodsCase records of 25 patients with Budd-Chiari syndrome were evaluated retrospectively. These patients were investigated with imaging techniques and underwent balloon angioplasty or… read more here.
Keywords: balloon angioplasty; budd chiari; chiari syndrome; case series ... See more keywords
Patients With Budd-Chiari Syndrome Have Variable Coagulation Status on Thromboelastography at Diagnosis.
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DOI: 10.1016/j.jceh.2018.10.002
Abstract: Background & aims Budd-Chiari Syndrome (BCS) is considered a thrombophilic state, and most patients with BCS have thrombophilic disorder. Liver dysfunction-related coagulopathy makes coagulation function unpredictable in BCS. Thromboelastography (TEG) assesses the dynamics, strength, and… read more here.
Keywords: coagulation; chiari syndrome; budd chiari; teg ... See more keywords
Endothelial JAK2V617F does not enhance liver lesions in mice with Budd-Chiari syndrome.
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DOI: 10.1016/j.jhep.2018.01.010
Abstract: To the Editor: Budd-Chiari syndrome is defined as hepatic venous outflow obstruction in the absence of congestive or restrictive heart disease. Myeloproliferative neoplasms are the leading cause of Budd-Chiari syndrome, diagnosed in 25–50% of such… read more here.
Keywords: endothelial jak2v617f; budd chiari; chiari syndrome; jak2v617f enhance ... See more keywords
Balloon venoplasty as primary modality of treatment in children with Budd-Chiari syndrome.
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DOI: 10.1016/j.jpedsurg.2020.05.021
Abstract: INTRODUCTION Budd-Chiari syndrome (BCS) is a rare condition affecting children. It is characterized by occlusion of venous outflow from liver at the level of hepatic veins (HV) or inferior vena cava (IVC). The management of… read more here.
Keywords: bcs; budd chiari; balloon venoplasty; chiari syndrome ... See more keywords
Non-contrast-enhanced MR angiography in the diagnosis of Budd-Chiari syndrome (BCS) compared with digital subtraction angiography (DSA): Preliminary results.
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DOI: 10.1016/j.mri.2016.10.006
Abstract: Non-CE MRA techniques (true steady-state free-precession, SSFP) have been used effectively for the selective visualization of the portal venous system and inferior vena cava. Budd-Chiari Syndrome (BCS) encompasses a number of conditions that cause the… read more here.
Keywords: obstruction; budd chiari; ivc obstruction; chiari syndrome ... See more keywords
Budd–Chiari syndrome associated to Behcet disease: An observational retrospective multicenter study in Morocco
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DOI: 10.1097/md.0000000000031308
Abstract: Budd–Chiari syndrome (BCS) is considered a rare but serious complication of Behçet’s disease (BD). This study was performed to define the prevalence, clinical and biological features, treatment, and clinical course of BSC associated with BD… read more here.
Keywords: disease; syndrome associated; budd chiari; chiari syndrome ... See more keywords
Liver Transplantation for Budd-Chiari Syndrome in the MELD Era
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DOI: 10.1097/txd.0000000000001407
Abstract: Background. To evaluate clinical characteristics and factors associated with survival among liver transplantation (LT) recipients with Budd-Chiari syndrome (BCS), with or without transjugular intrahepatic portosystemic shunt (TIPS), in the post–Model for End-stage Liver Disease era.… read more here.
Keywords: survival; budd chiari; bcs; transplantation ... See more keywords