Accumulation of prion protein in the vagus nerve in creutzfeldt–jakob disease
Sign Up to like & getrecommendations! Published in 2019 at "Annals of Neurology"
DOI: 10.1002/ana.25451
Abstract: Disease‐associated proteins are thought to propagate along neuronal processes in neurodegenerative diseases. To detect disease‐associated prion protein (PrPSc) in the vagus nerve in different forms and molecular subtypes of Creutzfeldt–Jakob disease (CJD), we applied 3… read more here.
Keywords: cjd; disease; jakob disease; vagus nerve ... See more keywords
Sporadic CJD in association with HIV
Sign Up to like & getrecommendations! Published in 2018 at "Journal of Neurology"
DOI: 10.1007/s00415-018-9116-0
Abstract: BackgroundCreutzfeldt-Jakob disease (CJD) is a rapidly progressive fatal neurodegenerative disorder. We report an unusual case of pathologically confirmed sporadic CJD developing in a HIV-positive patient but presenting with clinical and radiological features suggestive of variant… read more here.
Keywords: cjd; association; variant cjd; hiv sporadic ... See more keywords
Three cases of Creutzfeldt–Jakob disease presenting with a predominant dysexecutive syndrome
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Neurology"
DOI: 10.1007/s00415-022-11045-7
Abstract: Creutzfeldt–Jakob disease (CJD) is a rare, uniformly fatal prion disease. Although CJD commonly presents with rapidly progressive dementia, ataxia, and myoclonus, substantial clinicopathological heterogeneity is observed in clinical practice. Unusual and predominantly cognitive clinical manifestations… read more here.
Keywords: cjd; dysexecutive syndrome; creutzfeldt jakob; disease ... See more keywords
P 164 Parietal stroke mimicking the Heidenhain variant of Creutzfeldt-Jakob Disease
Sign Up to like & getrecommendations! Published in 2017 at "Clinical Neurophysiology"
DOI: 10.1016/j.clinph.2017.06.235
Abstract: The Heidenhain variant of Creutzfeldt-Jakob disease (CJD) is a rapidly progressive neurodegenerative disease with an occipito-parietal focus.It initially presents with visual disturbances such as visual agnosia or cortical blindness ( Kropp et al., 1999 ).After… read more here.
Keywords: heidenhain; cjd; disease; heidenhain variant ... See more keywords
Electroretinogram (ERGs) and visual evoked potentials (VEPs) study in prion disease (CJD)
Sign Up to like & getrecommendations! Published in 2019 at "Clinical Neurophysiology"
DOI: 10.1016/j.clinph.2018.09.079
Abstract: Literature reported on ERGs and VEPs changes in patients with prion disease (CJD). To characterize the extent of ERG and VEPs involvement in confirmed CJD; to assess ERGs and VEPs diagnostic usefulness in the workout… read more here.
Keywords: prion disease; disease cjd; ergs veps; cjd ... See more keywords
Second-Generation RT-QuIC Assay for the Diagnosis of Creutzfeldt-Jakob Disease Patients in Brazil
Sign Up to like & getrecommendations! Published in 2020 at "Frontiers in Bioengineering and Biotechnology"
DOI: 10.3389/fbioe.2020.00929
Abstract: The recent development of IQ-CSF, the second generation of real-time quaking-induced conversion (RT-QuIC) using cerebrospinal fluid (CSF), for the diagnosis of Creutzfeldt-Jakob Disease (CJD) represents a major diagnostic advance in the field. Highly accurate results… read more here.
Keywords: diagnosis; diagnosis creutzfeldt; cjd; csf ... See more keywords
Could Sporadic Creutzfeldt-Jakob Disease Be Underdiagnosed in China? Experience From Four Cases
Sign Up to like & getrecommendations! Published in 2020 at "Frontiers in Neurology"
DOI: 10.3389/fneur.2020.00763
Abstract: Background: Creutzfeldt-Jakob Disease (CJD) is a rapidly progressive neurodegenerative disease caused by the misfolded version of the cellular prion protein. Here we report four cases of sporadic CJD (sCJD) and describe the diagnostic methods available… read more here.
Keywords: cjd; disease; jakob disease; china ... See more keywords
Does the Use of Antidepressants Accelerate the Disease Progress in Creutzfeldt–Jakob Disease Patients With Depression? A Case Report and A Systematic Review
Sign Up to like & getrecommendations! Published in 2019 at "Frontiers in Psychiatry"
DOI: 10.3389/fpsyt.2019.00297
Abstract: Background: Creutzfeldt–Jakob disease (CJD) is a fatal neurodegenerative disorder characterized by rapidly progressive dementia. Growing evidence suggests that antidepressant usage was associated with dementia. Given the commonality of depression in CJD, it is necessary to… read more here.
Keywords: survival time; cjd; disease; case ... See more keywords
Genetic Risk Factors of Creutzfeldt-Jakob Disease in the Population of Newborns in Slovakia
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DOI: 10.3390/pathogens10040435
Abstract: The most frequent human prion disease is Creutzfeldt–Jakob disease (CJD). It occurs as sporadic (sCJD), genetic (gCJD), iatrogenic (iCJD) form and as variant CJD. The genetic form represents about 10–15% of confirmed cases worldwide, in… read more here.
Keywords: risk; cjd; jakob disease; creutzfeldt jakob ... See more keywords
Histotype-Dependent Oligodendroglial PrP Pathology in Sporadic CJD: A Frequent Feature of the M2C “Strain”
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DOI: 10.3390/v13091796
Abstract: In sporadic Creutzfeldt-Jakob disease, molecular subtypes are neuropathologically well identified by the lesioning profile and the immunohistochemical PrPd deposition pattern in the grey matter (histotypes). While astrocytic PrP pathology has been reported in variant CJD… read more here.
Keywords: oligodendroglial prp; cjd; pathology; strain ... See more keywords