Pharmacokinetics, surrogate efficacy and safety evaluations of a new human plasma-derived fibrinogen concentrate (FIB Grifols) in adult patients with congenital afibrinogenemia.
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DOI: 10.1016/j.thromres.2020.12.026
Abstract: BACKGROUND AND AIMS Congenital afibrinogenemia is a rare coagulation disorder resulting from a deficiency in fibrinogen. This study assessed the pharmacokinetics, surrogate efficacy and safety of FIB Grifols, a new human plasma-derived fibrinogen concentrate, to… read more here.
Keywords: plasma; congenital afibrinogenemia; surrogate efficacy; efficacy ... See more keywords
Pulmonary Thromboendarterectomy Requiring Cardiopulmonary Bypass and Deep Hypothermic Circulatory Arrest in a Patient With Congenital Afibrinogenemia.
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DOI: 10.1053/j.jvca.2020.04.020
Abstract: Abstract Congenital afibrinogenemia is a rare autosomal recessive hematologic disorder that results in coagulopathy due to the complete lack of fibrinogen production. While the common manifestation of the disease entails a bleeding diathesis, these patients… read more here.
Keywords: hypothermic circulatory; congenital afibrinogenemia; cardiopulmonary bypass; circulatory arrest ... See more keywords
A Novel Frameshift Mutation in the FGA Gene (c.196 delT) Leading to Congenital Afibrinogenemia
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DOI: 10.1097/mph.0000000000001658
Abstract: Background: Congenital afibrinogenemia is characterized by the absence of fibrinogen. Congenital fibrinogen disorders result from several mutations in FGA, FGB, or FGG. Their epidemiology is not well known. Observation: The present study reports on 2… read more here.
Keywords: afibrinogenemia; mutation fga; frameshift mutation; congenital afibrinogenemia ... See more keywords
CONGENITAL AFIBRINOGENEMIA COMPLICATED BY A PORTAL CAVERNOMA: ABOUT A CASE
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DOI: 10.21474/ijar01/10638
Abstract: 1. Service D’hépato-Gastroentérologie CHU Hassan II-Fès Service de radiologie CHU Hassan II Fès. 2. Faculté De Médecine et de Pharmacie de FèsUniversité sidi Mohammed ben AbdellahFès. ...................................................................................................................... Manuscript Info Abstract ......................... ........................................................................ Manuscript History Received:… read more here.
Keywords: afibrinogenemia complicated; complicated portal; congenital afibrinogenemia; cavernoma case ... See more keywords