Beyond the length and look of repolarization: Defining the non-QTc electrocardiographic profiles of patients with congenital long QT syndrome.
Sign Up to like & getrecommendations! Published in 2018 at "Heart rhythm"
DOI: 10.1016/j.hrthm.2018.04.033
Abstract: BACKGROUND Little is known about the spectrum and prevalence of ECG features beyond the length and morphology of repolarization in patients with congenital long QT syndrome (LQTS). OBJECTIVE The purpose of this study was to… read more here.
Keywords: lqts type; patients congenital; long syndrome; beyond length ... See more keywords
The congenital long QT syndrome Type 3: An update
Sign Up to like & getrecommendations! Published in 2018 at "Indian Pacing and Electrophysiology Journal"
DOI: 10.1016/j.ipej.2017.10.011
Abstract: Congenital long QT syndrome type 3 (LQT3) is the third in frequency compared to the 15 forms known currently of congenital long QT syndrome (LQTS). Cardiac events are less frequent in LQT3 when compared with… read more here.
Keywords: long syndrome; syndrome type; type update; congenital long ... See more keywords
CONGENITAL LONG QT SYNDROME TYPE 2: THE CASE OF A MISDIAGNOSED ARRHYTHMIA AND A NEAR FALL FROM DEATH
Sign Up to like & getrecommendations! Published in 2019 at "Journal of the American College of Cardiology"
DOI: 10.1016/s0735-1097(19)33535-1
Abstract: Long QT Syndrome-2 (LQT2) is a rare congenital disorder of ventricular myocardial repolarization due to heterozygous mutations in the alpha subunit of the rapid rectifier potassium channel of HERG and MiRP1 genes resulting in slowing… read more here.
Keywords: syndrome type; congenital long; long syndrome; case misdiagnosed ... See more keywords
Automated T‐wave analysis can differentiate acquired QT prolongation from congenital long QT syndrome
Sign Up to like & getrecommendations! Published in 2017 at "Annals of Noninvasive Electrocardiology"
DOI: 10.1111/anec.12455
Abstract: Prolongation of the QT on the surface electrocardiogram can be due to either genetic or acquired causes. Distinguishing congenital long QT syndrome (LQTS) from acquired QT prolongation has important prognostic and management implications. We aimed… read more here.
Keywords: long syndrome; wave analysis; acquired prolongation; congenital long ... See more keywords
Mutational spectrum of congenital long QT syndrome in Turkey; identification of 12 novel mutations across KCNQ1, KCNH2, SCN5A, KCNJ2, CACNA1C, and CALM1
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Cardiovascular Electrophysiology"
DOI: 10.1111/jce.15306
Abstract: Long QT syndrome (LQTS) is of great importance as it is the most common cause of sudden cardiac death in childhood. The diagnosis is made by the prolongation of the QTc interval on the electrocardiography.… read more here.
Keywords: long syndrome; spectrum congenital; syndrome turkey; congenital long ... See more keywords
Congenital long QT syndrome presenting as unexplained bradycardia
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DOI: 10.1136/bcr-2021-242362
Abstract: Congenital long QT syndrome (LQTS) is a genetically autosomal heterogeneous disorder of the ion channels and causes about 10% of sudden death infant syndrome in newborns. Its estimated prevalence is approximately 1 in 2500, probably… read more here.
Keywords: long syndrome; presenting unexplained; congenital long; unexplained bradycardia ... See more keywords
Congenital long QT syndrome and patent ductus arteriosus: A rare surgical scenario
Sign Up to like & getrecommendations! Published in 2021 at "Annals of Pediatric Cardiology"
DOI: 10.4103/apc.apc_146_19
Abstract: Congenital long QT syndrome (LQTS) is a rare cardiac condition characterized by abnormality of either sodium or potassium ion channels resulting in prolongation of QT interval and thereby predisposing to life-threatening arrhythmia. Once the syndrome… read more here.
Keywords: long syndrome; ductus arteriosus; congenital long; patent ductus ... See more keywords