Analysis of pulmonary features and treatment approaches in the COPA syndrome
Sign Up to like & getrecommendations! Published in 2018 at "ERJ Open Research"
DOI: 10.1183/23120541.00017-2018
Abstract: The COPA syndrome is a monogenic, autoimmune lung and joint disorder first identified in 2015. This study sought to define the main pulmonary features of the COPA syndrome in an international cohort of patients, analyse… read more here.
Keywords: treatment; copa syndrome; disease; pulmonary features ... See more keywords
COPA Syndrome—From Pathogenesis to Treatment
Sign Up to like & getrecommendations! Published in 2024 at "Diagnostics"
DOI: 10.3390/diagnostics14242819
Abstract: Coatomer subunit α (COPA) syndrome is a mendelian autosomal dominant immune dysregulation disease characterized by early onset lung disease in the form of diffuse alveolar hemorrhaging or interstitial lung disease, frequently associated with arthritis, glomerulonephritis,… read more here.
Keywords: copa syndrome; disease; pathogenesis treatment; lung disease ... See more keywords