Validation of Revised International Creutzfeldt-Jakob Disease Surveillance Network Diagnostic Criteria for Sporadic Creutzfeldt-Jakob Disease
Sign Up to like & getrecommendations! Published in 2022 at "JAMA Network Open"
DOI: 10.1001/jamanetworkopen.2021.46319
Abstract: Key Points Question How sensitive and specific are the 2017 revised International Creutzfeldt-Jakob disease Surveillance Network diagnostic criteria for the diagnosis of sporadic Creutzfeldt-Jakob disease? Findings In this diagnostic study of 647 individuals conducted by… read more here.
Keywords: creutzfeldt jakob; jakob disease; diagnostic criteria;
Prevention of Creutzfeldt-Jakob Disease in Patients Undergoing Surgery.
Sign Up to like & getrecommendations! Published in 2022 at "JAMA network open"
DOI: 10.1001/jamanetworkopen.2022.1561
Abstract: assess the potential for iatrogenic transmission of the rare but devastating Creutzfeldt-Jakob disease (CJD) through surgical procedures prior to CJD diagnosis. The authors performed a retrospective analysis of 121 patients with probable or definite CJD… read more here.
Keywords: creutzfeldt jakob; jakob disease; prevention creutzfeldt;
Analysis of Clinical Features, Diagnostic Tests, and Biomarkers in Patients With Suspected Creutzfeldt-Jakob Disease, 2014-2021
Sign Up to like & getrecommendations! Published in 2022 at "JAMA Network Open"
DOI: 10.1001/jamanetworkopen.2022.25098
Abstract: Key Points Question What is the diagnostic utility associated with clinical features and tests historically associated with Creutzfeldt-Jakob disease (CJD) in patients evaluated in the modern era? Findings In this cohort study including 115 patients,… read more here.
Keywords: creutzfeldt jakob; jakob disease; patients suspected; clinical features ... See more keywords
Accumulation of prion protein in the vagus nerve in creutzfeldt–jakob disease
Sign Up to like & getrecommendations! Published in 2019 at "Annals of Neurology"
DOI: 10.1002/ana.25451
Abstract: Disease‐associated proteins are thought to propagate along neuronal processes in neurodegenerative diseases. To detect disease‐associated prion protein (PrPSc) in the vagus nerve in different forms and molecular subtypes of Creutzfeldt–Jakob disease (CJD), we applied 3… read more here.
Keywords: cjd; disease; jakob disease; vagus nerve ... See more keywords
Default Mode Network quantitative diffusion and resting‐state functional magnetic resonance imaging correlates in sporadic Creutzfeldt‐Jakob disease
Sign Up to like & getrecommendations! Published in 2022 at "Human Brain Mapping"
DOI: 10.1002/hbm.25945
Abstract: Grey matter involvement is a well‐known feature in sporadic Creutzfeldt–Jakob disease (sCJD), yet precise anatomy‐based quantification of reduced diffusivity is still not fully understood. Default Mode Network (DMN) areas have been recently demonstrated as selectively… read more here.
Keywords: disease; creutzfeldt jakob; sporadic creutzfeldt; diffusivity ... See more keywords
Creutzfeldt–Jakob Disease Misdiagnosed as Multiple System Atrophy
Sign Up to like & getrecommendations! Published in 2023 at "Movement Disorders Clinical Practice"
DOI: 10.1002/mdc3.13654
Abstract: Multiple system atrophy (MSA) is a progressive neurodegenerative disorder characterized by various combinations of autonomic failure, parkinsonism, and cerebellar syndromes. Although consensus criteria have been widely used to diagnose MSA, accurate clinical diagnosis remains challenging.… read more here.
Keywords: creutzfeldt jakob; jakob disease; multiple system; system atrophy ... See more keywords
Prognostic value of diffusion-weighted imaging in patients with newly diagnosed sporadic Creutzfeldt-Jakob disease
Sign Up to like & getrecommendations! Published in 2021 at "European Radiology"
DOI: 10.1007/s00330-021-08363-1
Abstract: Objectives To evaluate clinico-radiologic markers that predict poor overall survival (OS) in sporadic Creutzfeldt-Jakob disease (sCJD) and to develop a prognostic model. Materials and methods Patients with newly diagnosed sCJD were included who underwent diffusion-weighted… read more here.
Keywords: risk; creutzfeldt jakob; diffusion; sporadic creutzfeldt ... See more keywords
Diagnostic value of surrogate CSF biomarkers for Creutzfeldt–Jakob disease in the era of RT-QuIC
Sign Up to like & getrecommendations! Published in 2019 at "Journal of Neurology"
DOI: 10.1007/s00415-019-09537-0
Abstract: Prion real-time quaking-induced conversion (RT-QuIC) is emerging as the most potent assay for the in vivo diagnosis of Creutzfeldt–Jakob disease (CJD), but its full application, especially as a screening test, is limited by suboptimal substrate… read more here.
Keywords: diagnosis; surrogate; csf; jakob disease ... See more keywords
Three cases of Creutzfeldt–Jakob disease presenting with a predominant dysexecutive syndrome
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Neurology"
DOI: 10.1007/s00415-022-11045-7
Abstract: Creutzfeldt–Jakob disease (CJD) is a rare, uniformly fatal prion disease. Although CJD commonly presents with rapidly progressive dementia, ataxia, and myoclonus, substantial clinicopathological heterogeneity is observed in clinical practice. Unusual and predominantly cognitive clinical manifestations… read more here.
Keywords: cjd; dysexecutive syndrome; creutzfeldt jakob; disease ... See more keywords
The risk of Creutzfeldt–Jakob disease infection in cadaveric surgical training
Sign Up to like & getrecommendations! Published in 2022 at "Anatomical Science International"
DOI: 10.1007/s12565-022-00662-x
Abstract: The usefulness of cadaver surgical training in the clinical field is already well known. In Japan, the number of universities introducing cadaver surgical training is increasing. In addition to formalin fixation, various fixation methods are… read more here.
Keywords: creutzfeldt jakob; cadaver surgical; prion diseases; surgical training ... See more keywords
Atypical presentation of probable Creutzfeldt-Jakob disease associated with anti-Zic4 antibody: Literature review of neuronal antibodies in Creutzfeldt-Jakob disease
Sign Up to like & getrecommendations! Published in 2018 at "Clinical Neurology and Neurosurgery"
DOI: 10.1016/j.clineuro.2018.02.043
Abstract: INTRODUCTION Sporadic Creutzfeldt-Jakob disease is a prion disease characterized by rapidly progressive dementia, ataxia and myoclonus. Atypical phenotype masquerading as stroke, movement disorders or autoimmune encephalitis have been described. Here, I report a probable case… read more here.
Keywords: anti zic4; disease; jakob disease; neuronal antibodies ... See more keywords