Trends in erythrocyte protoporphyrin IX concentration by age, sex and season among patients with erythropoietic protoporphyria - 20 years of follow-up.
Sign Up to like & getrecommendations! Published in 2020 at "Photodiagnosis and photodynamic therapy"
DOI: 10.1016/j.pdpdt.2020.101928
Abstract: BACKGROUND Erythropoietic protoporphyria (EPP) is an inherited disorder leading to an increased concentration of the photoactive protoporphyrin IX (PpIX) in erythrocytes. Upon photoactivation in the dermal blood vessels and release to the skin it causes… read more here.
Keywords: erythrocyte ppix; erythropoietic protoporphyria; age; ppix ... See more keywords
Cimetidine for erythropoietic protoporphyria.
Sign Up to like & getrecommendations! Published in 2022 at "Photodiagnosis and photodynamic therapy"
DOI: 10.1016/j.pdpdt.2022.102793
Abstract: BACKGROUND Erythropoietic protoporphyria (EPP) is caused by deficiency of the enzyme converting protoporphyrin IX (PpIX) into heme resulting in accumulation of PpIX leading to photosensitivity and liver toxicity. Cimetidine might inhibit δ-aminolevulinic acid synthase influencing… read more here.
Keywords: treated cimetidine; treatment; photosensitivity; erythrocyte ppix ... See more keywords