Comparative analysis of right ventricular strain in Fabry cardiomyopathy and sarcomeric hypertrophic cardiomyopathy
Sign Up to like & getrecommendations! Published in 2022 at "European Heart Journal Cardiovascular Imaging"
DOI: 10.1093/ehjci/jeac151
Abstract: Abstract Aims To perform a comparative analysis of right ventricle (RV) myocardial mechanics, assessed by 2D speckle-tracking echocardiography (2D-STE), between patients with Fabry disease and patients with sarcomeric disease. Methods and results Patients with Fabry… read more here.
Keywords: comparative analysis; fabry cardiomyopathy; analysis right; cardiomyopathy ... See more keywords
P899Long-term evolution of Fabry cardiomyopathy under enzyme replacement therapy in the Swiss Fabry cohort. An echocardiographic study
Sign Up to like & getrecommendations! Published in 2019 at "European Heart Journal"
DOI: 10.1093/eurheartj/ehz747.0495
Abstract: Fabry cardiomyopathy may present with left ventricular hypertrophy (LVH) and enzyme replacement therapy (ERT) aims to slow its progression in affected patients. LVH progression may be observed despite ERT and the aim of this study… read more here.
Keywords: mass; increase; study; fabry cardiomyopathy ... See more keywords
Early stage Fabry cardiomyopathy misdiagnosed as perimyocarditis
Sign Up to like & getrecommendations! Published in 2023 at "Journal of Cardiovascular Medicine"
DOI: 10.2459/jcm.0000000000001405
Abstract: A 56-year-old Caucasian woman was admitted to our ICU department because of chest pain and worsening dyspnea. Three months before, she had been admitted to a peripheric hospital for chest pain and high troponin levels.… read more here.
Keywords: misdiagnosed perimyocarditis; fabry cardiomyopathy; early stage; stage fabry ... See more keywords