Diagnostic Utility of PRAME in Rare Melanoma Mimics: A Comparative Analysis Including GNET, MMNST, Epithelioid MPNST, and MITFâRearranged Melanocytic Tumors
Sign Up to like & getrecommendations! Published in 2025 at "Journal of Cutaneous Pathology"
DOI: 10.1111/cup.14849
Abstract: Differentiating metastatic melanoma from histologic mimics such as malignant gastrointestinal neuroectodermal tumor (GNET), malignant melanotic nerve sheath tumor (MMNST), and epithelioid malignant peripheral nerve sheath tumor (EMPNST) poses significant diagnostic challenges due to overlapping morphology… read more here.
Keywords: mmnst epithelioid; gnet; melanoma mimics; melanoma ... See more keywords
Gastrointestinal Neuroectodermal Tumor/Extraskeletal Ewing Sarcoma of the Ileum with Ulcerative Colitis
Sign Up to like & getrecommendations! Published in 2024 at "Case Reports in Gastroenterology"
DOI: 10.1159/000542659
Abstract: Abstract Introduction Malignant gastrointestinal neuroectodermal tumor (GNET), previously known as clear cell sarcoma-like tumor of the gastrointestinal tract, is an extremely rare and aggressive mesenchymal neoplasm characterized by high rates of recurrence, metastases, and mortality.… read more here.
Keywords: gnet; gastrointestinal neuroectodermal; tumor; ulcerative colitis ... See more keywords
The Role of Targeted Therapy and Immunotherapy in Metastatic GNET/Clear Cell Sarcoma (CCS) of the Gastrointestinal Tract: A Case Report
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DOI: 10.3390/cimb47090706
Abstract: Background: Gastrointestinal neuroectodermal tumour (GNET), also known as clear cell sarcoma (CCS) of the gastrointestinal tract, is a rare neural crest-derived malignancy characterized by EWSR1-ATF1 or EWSR1-CREB1 fusions. Due to its rarity, there is limited… read more here.
Keywords: gnet; cell sarcoma; targeted therapy; case ... See more keywords
A Case Series of Metastatic Malignant Gastrointestinal Neuroectodermal Tumors and Comprehensive Genomic Profiling Analysis of 20 Cases
Sign Up to like & getrecommendations! Published in 2022 at "Current Oncology"
DOI: 10.3390/curroncol29020109
Abstract: Malignant gastrointestinal neuroectodermal tumor (GNET) is an ultra-rare soft tissue sarcoma, therefore often misdiagnosed and has no available standard treatment. Here, we report 3 cases of metastatic GNET with variable clinical courses. Our small case… read more here.
Keywords: case series; gastrointestinal neuroectodermal; malignant gastrointestinal; comprehensive genomic ... See more keywords