Efficacy and safety of erythrocytapheresis and low‐dose erythropoietin for treatment of hemochromatosis
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Clinical Apheresis"
DOI: 10.1002/jca.21477
Abstract: The aim of this study was to determine retrospectively the efficacy of combined therapy using erythropoietin (EPO) and erythrocytapheresis (EA) in patients with hereditary hemochromatosis (HH) who did not tolerate phlebotomy. read more here.
Keywords: efficacy safety; hemochromatosis; efficacy; erythrocytapheresis low ... See more keywords
Chelating Polymers for Hereditary Hemochromatosis Treatment.
Sign Up to like & getrecommendations! Published in 2020 at "Macromolecular bioscience"
DOI: 10.1002/mabi.202000254
Abstract: Hemochromatosis (iron overload) encompasses a group of diseases that are characterized by a toxic hyperaccumulation of iron in parenchymal organs. Currently, only few treatments for this disease have been approved; however, all these treatments possess… read more here.
Keywords: gastrointestinal tract; chelating polymers; polymers hereditary; treatment ... See more keywords
Clinicopathological diagnosis and treatment of juvenile hemochromatosis
Sign Up to like & getrecommendations! Published in 2019 at "Chinese Medical Journal"
DOI: 10.1097/cm9.0000000000000547
Abstract: His serum ferritin concentration was 8729.2 ng/mL, with a To the Editor:Hereditary hemochromatosis (HH) is a lateonset autonomic disease characterized by enhanced transferrin saturation of 112.4%. intestinal absorption of iron and iron overload, which may… read more here.
Keywords: diagnosis treatment; juvenile hemochromatosis; hemochromatosis; gene ... See more keywords
Autopsy relevance determining hemochromatosis
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DOI: 10.1097/md.0000000000008788
Abstract: Rationale: Hemochromatosis is a disorder, associated with an abnormal accumulation of iron leading to toxic organ damage. Clinical symptoms develop during a long period of time, thus, determining accidental or late diagnosis, usually when complications… read more here.
Keywords: medicine; hemochromatosis; autopsy; relevance determining ... See more keywords
Proposed dietary recommendations for iron overload: a guide for physician practice
Sign Up to like & getrecommendations! Published in 2023 at "Current Opinion in Gastroenterology"
DOI: 10.1097/mog.0000000000000923
Abstract: Purpose of review Iron overload disorders such as hemochromatosis involve unregulated absorption of dietary iron, leading to excessive iron accumulation in multiple organs. Phlebotomy is the standard of care for removal of excess iron, but… read more here.
Keywords: practice; iron overload; iron; guide ... See more keywords
Comparing Care of the Primary and Secondary Hemochromatosis Patients
Sign Up to like & getrecommendations! Published in 2020 at "Journal of Infusion Nursing"
DOI: 10.1097/nan.0000000000000358
Abstract: Hemochromatosis is an imbalance of excessive serum iron and is a life-threatening condition if left untreated. Due to different causes, primary and secondary hemochromatosis have different patient care considerations for the infusion nurse. Understanding the… read more here.
Keywords: care; secondary hemochromatosis; primary secondary; hemochromatosis ... See more keywords
Long-term Outcome of Orthotopic Liver Transplantation in Patients With Hemochromatosis: A Summary of a 30-year Transplant Program
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DOI: 10.1097/txd.0000000000001007
Abstract: Background. Hemochromatosis (HC) is an autosomal recessive disease characterized by impaired iron metabolism and a rare indication for orthotopic liver transplantation (LT). Data about iron reaccumulation and remodeling of the liver graft after LT are… read more here.
Keywords: hemochromatosis; transplantation; long term; orthotopic liver ... See more keywords
Remembering Lawrie Powell 1934–2022
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Gastroenterology and Hepatology"
DOI: 10.1111/jgh.16031
Abstract: Professor Lawrie Powell passed away peacefully on September 23, 2022, aged 87. While best known internationally as THE world authority on the iron-storage disorder, hemochromatosis, and in Australia as the Father of Australian Hepatology, Lawrie… read more here.
Keywords: gastroenterology; hemochromatosis; hepatology; lawrie powell ... See more keywords
FRI0596 Feasibility of joint structural analysis in hemochromatosis hand arthropathy using high-resolution peripheral quantitative computed tomography – first results and clinical correlations
Sign Up to like & getrecommendations! Published in 2018 at "Annals of the Rheumatic Diseases"
DOI: 10.1136/annrheumdis-2018-eular.4903
Abstract: Background Hereditary Hemochromatosis (HH) is a common inherited disorder and characterised by an excess iron accumulation in several organs with consecutive organ dysfunction.1 Apart from the liver, the joints are a major site of excess… read more here.
Keywords: resolution; space; space width; hemochromatosis ... See more keywords
Reversal of end-stage heart failure in juvenile hemochromatosis with iron chelation therapy: a case report
Sign Up to like & getrecommendations! Published in 2018 at "Journal of Medical Case Reports"
DOI: 10.1186/s13256-017-1526-6
Abstract: BackgroundJuvenile hemochromatosis is the most severe form of iron overloading phenotype. Although rare, it should be suspected in patients who present with hypogonadotropic hypogonadism, diabetes mellitus, or cardiomyopathy without a clear cause.Case presentationA young Serbian… read more here.
Keywords: stage heart; hemochromatosis; case; iron ... See more keywords
Hereditary hemochromatosis beyond hyperferritinemia: Clinical and laboratory investigation of the patient’s profile submitted to phlebotomy in two reference centers in southern Brazil
Sign Up to like & getrecommendations! Published in 2023 at "Genetics and Molecular Biology"
DOI: 10.1590/1678-4685-gmb-2022-0230
Abstract: Abstract Hereditary Hemochromatosis is a disorder characterized by iron deposition in several organs and hyperferritinemia. The most studied variants are linked to the HFE gene. In Brazil, surveys that characterize this population are scarce, with… read more here.
Keywords: hereditary hemochromatosis; beyond hyperferritinemia; hemochromatosis beyond; hemochromatosis ... See more keywords