Erratum to: Subacute onset Hirayama disease with extensive myelopathy on MRI in flexed posture
Sign Up to like & getrecommendations! Published in 2017 at "Acta Neurologica Belgica"
DOI: 10.1007/s13760-017-0789-4
Abstract: Our case is an exceptional illustration of the proposed flexion-induced pathophysiology of Hirayama disease. Evidence, privileging a mechanical pathophysiology, is growing and diagnostic inclusion criteria are involving MRI-confirmed evidence of the mechanical pathophysiology. The forward… read more here.
Keywords: disease; myelopathy; mri; hirayama disease ... See more keywords
Serum cytokine and chemokine profiles in patients with juvenile muscular atrophy of distal upper extremity (Hirayama disease)
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Neuroimmunology"
DOI: 10.1016/j.jneuroim.2016.11.011
Abstract: Juvenile muscular atrophy of the distal upper extremity (Hirayama disease) is characterized by adolescent-onset muscular weakness of the distal upper limb. Several studies showed the contribution of atopic disposition and hyperIgEaemia to the disease process,… read more here.
Keywords: juvenile muscular; distal upper; disease; muscular atrophy ... See more keywords
Spinal Epidural Venous Plexus Pathology in Hirayama Disease.
Sign Up to like & getrecommendations! Published in 2019 at "Journal of Clinical Neuromuscular Disease"
DOI: 10.1097/cnd.0000000000000243
Abstract: Hirayama disease is a rare juvenile amyotrophy that is often misdiagnosed as an unrelated, relentlessly progressive disease. We present the case of an 18-year-old man who presented with weakness and atrophy of the right forearm… read more here.
Keywords: hirayama disease; pathology; venous plexus; disease ... See more keywords
Clinical profile and dynamic magnetic resonance imaging in Hirayama disease: a single-centered cross-sectional study in Nepal
Sign Up to like & getrecommendations! Published in 2023 at "Annals of Medicine and Surgery"
DOI: 10.1097/ms9.0000000000000664
Abstract: Introduction: Hirayama disease (HD) is juvenile monomelic amyotrophy of the distal upper limb first described by Hirayama in 1959 AD. HD is a benign condition with chronic microcirculatory changes. The hallmark of HD is necrosis… read more here.
Keywords: disease; cord atrophy; hirayama disease; extension ... See more keywords
Polymyoclonus aggravated by neck flexion as the isolated presenting symptom of Hirayama disease: case report
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DOI: 10.1186/s12883-020-01904-z
Abstract: Background We report a rare case of an 18-year-old male with unilateral hand tremor who was finally diagnosed with Hirayama disease (HD). Case presentation An 18-year-old male presented with unilateral polymyoclonus that aggravated with neck… read more here.
Keywords: polymyoclonus; flexion; disease; case ... See more keywords
How to reconstruct the lordosis of cervical spine in patients with Hirayama disease? A finite element analysis of biomechanical changes focusing on adjacent segments after anterior cervical discectomy and fusion
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Orthopaedic Surgery and Research"
DOI: 10.1186/s13018-022-02984-y
Abstract: Purpose To compare the biomechanical changes of adjacent segments between patients with Hirayama disease and non-pathological people after anterior cervical discectomy and fusion (ACDF) operation, and to explore the optimal degree of local lordosis reconstruction… read more here.
Keywords: lordosis; adjacent segments; patients hirayama; cervical spine ... See more keywords
The Importance of Flexion MRI in Hirayama Disease with Special Reference to Laminodural Space Measurements
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DOI: 10.3174/ajnr.a5577
Abstract: BACKGROUND AND PURPOSE: Hirayama disease is a benign focal amyotrophy of the distal upper limbs involving C7, C8, and T1 segmental myotomes with sparing of the brachioradialis and proximal muscles of the upper limb innervated… read more here.
Keywords: hirayama disease; flexion; laminodural space;
Update on the Pathogenesis, Clinical Diagnosis, and Treatment of Hirayama Disease
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DOI: 10.3389/fneur.2021.811943
Abstract: Hirayama disease (HD) is characterized by the juvenile onset of unilateral or asymmetric weakness and amyotrophy of the hand and ulnar forearm and is most common in males in Asia. A perception of compliance with… read more here.
Keywords: diagnosis treatment; treatment; hirayama disease;
The radiological and electrophysiological characteristics of Hirayama disease with proximal involvement: A retrospective study
Sign Up to like & getrecommendations! Published in 2022 at "Frontiers in Neurology"
DOI: 10.3389/fneur.2022.969484
Abstract: Purpose Hirayama disease (HD) has been largely believed to affect only distal muscles. However, the proximal upper extremities have been affected in some cases, which can be confused with motor neuron diseases. Methods Baseline data,… read more here.
Keywords: patients proximal; proximal involvement; hirayama disease; proximal group ... See more keywords