[Acquired C1 esterase inhibitor deficiency via bradykinin-mediated angioedema: Four cases].
Sign Up to like & getrecommendations! Published in 2018 at "Annales de dermatologie et de venereologie"
DOI: 10.1016/j.annder.2018.02.012
Abstract: BACKGROUND Acquired C1-esterase inhibitor (C1-INH) deficiency angioedema (C1-INH-AAE) is a form of bradykinin-mediated angioedema. This rare disorder is due to acquired consumption of C1-INH, hyperactivation of the classic pathway of human complement, and potentially fatal… read more here.
Keywords: inh aae; acquired esterase; esterase inhibitor; mediated angioedema ... See more keywords
Where we are with acquired angioedema due to C1 inhibitor deficiency: A systematic literature review.
Sign Up to like & getrecommendations! Published in 2021 at "Clinical immunology"
DOI: 10.1016/j.clim.2021.108819
Abstract: Acquired angioedema due to C1 inhibitor deficiency (C1-INH-AAE) is a rare disease characterized by adult-onset recurrent non-urticarial angioedema with low levels of C1-INH. It is associated with lymphoproliferative disorders, and treatments are off-label with variable… read more here.
Keywords: inh aae; angioedema due; inhibitor deficiency; acquired angioedema ... See more keywords
Idiopathic non-histaminergic acquired angioedema: a case series and discussion of published clinical trials
Sign Up to like & getrecommendations! Published in 2017 at "Clinical and Translational Allergy"
DOI: 10.1186/s13601-017-0164-9
Abstract: AbstractBackgroundIdiopathic non-histaminergic acquired angioedema (InH-AAE) is a rare disease for which there are no available laboratory parameters to clearly define the disorder. Therapy is often difficult and various treatment options have been proposed. In this… read more here.
Keywords: inh aae; response; non histaminergic; case ... See more keywords