Complement factor C4 activation in patients with hereditary angioedema.
Sign Up to like & getrecommendations! Published in 2017 at "Clinical biochemistry"
DOI: 10.1016/j.clinbiochem.2017.04.007
Abstract: OBJECTIVES Low complement factor C4 is usually considered a valuable screening tool for patients with the potentially life-threatening hereditary angioedema with C1-inhibitor (C1-INH) deficiency (C1-INH-HAE). However, there are patients with C1-INH-HAE presenting with normal C4… read more here.
Keywords: total antigenic; hae patients; non functional; hae ... See more keywords
Hereditary angioedema attack: what happens to vasoactive mediators?
Sign Up to like & getrecommendations! Published in 2019 at "International immunopharmacology"
DOI: 10.1016/j.intimp.2019.106079
Abstract: Hereditary angioedema is a disabling, life-threatening condition caused by deficiency (type I) or dysfunction (type II) of the C1 inhibitor protein (C1-INH-HAE) leading to bradykinin accumulation and recurrent episodes of edema attack. Vascular leakage is… read more here.
Keywords: attack; remission; vasoactive mediators; patients inh ... See more keywords
Psychometric study of the SF-36v2 in hereditary angioedema due to C1 inhibitor deficiency (C1-INH-HAE)
Sign Up to like & getrecommendations! Published in 2022 at "Orphanet Journal of Rare Diseases"
DOI: 10.1186/s13023-022-02202-2
Abstract: Background The generic 36-item Short-Form Health Survey (SF-36v2) has been used to assess health related quality of life in adult patients with hereditary angioedema due to C1-inhibitor deficiency (C1-INH-HAE) even though it has not yet… read more here.
Keywords: inhibitor deficiency; due inhibitor; inh hae; hereditary angioedema ... See more keywords
Secreted Phospholipases A2 in Hereditary Angioedema With C1-Inhibitor Deficiency
Sign Up to like & getrecommendations! Published in 2018 at "Frontiers in Immunology"
DOI: 10.3389/fimmu.2018.01721
Abstract: Background Hereditary angioedema (HAE) caused by deficiency (type I) or dysfunction (type II) of the C1 inhibitor protein (C1-INH-HAE) is a disabling, potentially fatal condition characterized by recurrent episodes of swelling. We have recently found… read more here.
Keywords: hgiia; inhibitor; permeability; inh hae ... See more keywords