Where we are with acquired angioedema due to C1 inhibitor deficiency: A systematic literature review.
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DOI: 10.1016/j.clim.2021.108819
Abstract: Acquired angioedema due to C1 inhibitor deficiency (C1-INH-AAE) is a rare disease characterized by adult-onset recurrent non-urticarial angioedema with low levels of C1-INH. It is associated with lymphoproliferative disorders, and treatments are off-label with variable… read more here.
Keywords: inh aae; angioedema due; inhibitor deficiency; acquired angioedema ... See more keywords
Intestinal angioedema caused by an acquired C1 esterase inhibitor deficiency associated with underlying splenic marginal zone lymphoma
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DOI: 10.1080/08998280.2021.1885277
Abstract: Abstract A 75-year-old woman presented with recurrent abdominal pain and vomiting for 1 year and was later found to have splenomegaly and pancytopenia. This case report depicts a clinical picture of intestinal angioedema, a challenging… read more here.
Keywords: intestinal angioedema; acquired esterase; deficiency associated; esterase inhibitor ... See more keywords
Icatibant for the treatment of hereditary angioedema with C1-inhibitor deficiency in adolescents and in children aged over 2 years
Sign Up to like & getrecommendations! Published in 2018 at "Expert Review of Clinical Immunology"
DOI: 10.1080/1744666x.2018.1476851
Abstract: ABSTRACT Introduction: Hereditary angioedema (HAE) due to C1-inhibitor deficiency (C1-INH-HAE) is a rare disorder with life-threatening complications if untreated. It begins during childhood, and reduces the patient’s quality of life. Therefore, the availability of an… read more here.
Keywords: aged years; treatment; hereditary angioedema; inhibitor deficiency ... See more keywords
Pediatric Emergency Department Management of C1 Inhibitor Deficiency
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DOI: 10.1097/pec.0000000000002443
Abstract: Introduction C1 inhibitor deficiency is a rare, potentially life-threatening syndrome. Acute attacks of angioedema may occur at any time, so the emergency department (ED) constitutes an indispensable component of its care. Aim To describe the… read more here.
Keywords: emergency department; inhibitor; inhibitor deficiency; management ... See more keywords
Presentation of an extraordinary colic: abdominal pain as the first and only utterance of an acquired C1-inhibitor deficiency
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DOI: 10.1136/bcr-2022-250710
Abstract: C1-inhibitor deficiency is a rare disease which incorporates acute self-limiting intermittent swelling of the subcutaneous tissue and mucous membranes. Attacks most frequently affect the face and/or the upper airway. Isolated angioedema of the small bowel… read more here.
Keywords: abdominal pain; first utterance; inhibitor deficiency; utterance acquired ... See more keywords
Psychometric study of the SF-36v2 in hereditary angioedema due to C1 inhibitor deficiency (C1-INH-HAE)
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DOI: 10.1186/s13023-022-02202-2
Abstract: Background The generic 36-item Short-Form Health Survey (SF-36v2) has been used to assess health related quality of life in adult patients with hereditary angioedema due to C1-inhibitor deficiency (C1-INH-HAE) even though it has not yet… read more here.
Keywords: inhibitor deficiency; due inhibitor; inh hae; hereditary angioedema ... See more keywords
Multicentric Observational Study on Safety and Tolerability of COVID-19 Vaccines in Patients with Angioedema with C1 Inhibitor Deficiency: Data from Italian Network on Hereditary and Acquired Angioedema (ITACA)
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DOI: 10.3390/vaccines11040852
Abstract: Angioedema due to C1 inhibitor deficiency (AE-C1-INH) is a rare disease characterized by recurrent and unpredictable attacks of angioedema. Multiple trigger factors, including trauma, emotional stress, infectious diseases, and drugs, could elicit angioedema attacks. The… read more here.
Keywords: inhibitor deficiency; tolerability covid; covid vaccines; study ... See more keywords