Acute Liver Failure due to Disseminated Juvenile Xanthogranuloma
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DOI: 10.1007/s12098-020-03389-7
Abstract: A 2-mo-old girl had hepatosplenomegaly and liver dysfunction (direct bilirubin level: 12.2 mg/dl, aspartate transaminase level: 202 IU/L, alanine aminotransferase level: 147 IU/L) with ascites since birth (Fig. 1a). When the patient developed brown rashes… read more here.
Keywords: liver failure; jxg; liver; juvenile xanthogranuloma ... See more keywords
Refractory Extracutaneous Juvenile Xanthogranuloma With Multiple Intracranial Nodular Lesions Successfully Treated With 2-Chlorodeoxyadenosine
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Pediatric Hematology/Oncology"
DOI: 10.1097/mph.0000000000002310
Abstract: Juvenile xanthogranulomatosis (JXG) is a rare histiocytic disease that is usually limited to the skin, but some JXG cases involve other organs. JXG involving the central nervous system (CNS) is rare and its treatment is… read more here.
Keywords: jxg; multiple intracranial; treated chlorodeoxyadenosine; jxg involving ... See more keywords
An unusual presentation of giant juvenile xanthogranuloma in a 9-year-old child
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DOI: 10.1136/archdischild-2022-324421
Abstract: A previously healthy 9yearold boy presented to dermatology outpatient clinic with a 2month history of an enlarging nodule on the anterior right shoulder (figure 1). There were no specific symptoms, family history or relevant medical… read more here.
Keywords: dermatology; juvenile xanthogranuloma; giant juvenile; jxg ... See more keywords
Histiocytic Disorders of Childhood.
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DOI: 10.1542/pir.2021-005367
Abstract: Histiocytic disorders of childhood represent a wide spectrum of conditions that share the common histologic feature of activated or transformed "histiocytes." Langerhans cell histiocytosis (LCH) is the most common, with an incidence of approximately 5… read more here.
Keywords: histiocytic disorders; disease; disorders childhood; rdd ... See more keywords