The “sweet spot” for maple syrup production proposed by is not that sweet
Sign Up to like & getrecommendations! Published in 2020 at "Forest Ecology and Management"
DOI: 10.1016/j.foreco.2019.117662
Abstract: Abstract In their paper recently published in FEM (“Finding the sweet spot: Shifting climate optima for maple syrup production in North America”), Rapp et al. (2019) suggest that there is a marked “sweet spot” for… read more here.
Keywords: sweet spot; maple syrup; syrup production; maple ... See more keywords
Authentication and quality control determination of maple syrup: A comprehensive review
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Food Composition and Analysis"
DOI: 10.1016/j.jfca.2021.103901
Abstract: Abstract Maple syrup a natural sweetener is obtained by boiling the sap drained from Acer saccharum L. tree and other maple species. Worldwide, maple syrup is produced only in Northeastern America, primarily in the province… read more here.
Keywords: maple syrup; authentication; quality control; maple ... See more keywords
A maple syrup extract alleviates liver injury in type 2 diabetic model mice.
Sign Up to like & getrecommendations! Published in 2019 at "Nutrition research"
DOI: 10.1016/j.nutres.2019.10.006
Abstract: A recent study showed that 54% of type 2 diabetes (T2D) patients have nonalcoholic fatty liver disease, which is a risk factor for aggravation diabetic symptoms. Previous studies suggested components in maple syrup alleviated liver… read more here.
Keywords: liver injury; syrup extract; maple syrup; mice ... See more keywords
Pathogenic Homozygous Mutations in the DBT Gene (c.1174A>C) Result in Maple Syrup Urine Disease in a rs12021720 Carrier.
Sign Up to like & getrecommendations! Published in 2022 at "Laboratory medicine"
DOI: 10.1093/labmed/lmac034
Abstract: OBJECTIVE Maple syrup urine disease (MSUD; OMIM #248600) is an autosomal recessive metabolic disorder in the catabolism of branched-chain amino acids (leucine, isoleucine, and valine) and may be lethal if untreated in affected newborns. METHODS… read more here.
Keywords: maple syrup; syrup urine; pathogenic homozygous; dbt gene ... See more keywords
Multi-Modal Sensing Platform for Continuous Analysis of Maple Syrup in Production Process
Sign Up to like & getrecommendations! Published in 2021 at "IEEE Sensors Journal"
DOI: 10.1109/jsen.2020.3014233
Abstract: In this work, we propose a new multimodal method/platform for continuous maple syrup °Brix monitoring and color grading during the production process. It is based on different detection methods such as electrical impedance, electrochemical sensing… read more here.
Keywords: grade; production process; platform continuous; maple syrup ... See more keywords
Long‐term results of liver transplantation for maple syrup urine disease: A single‐center experience in Turkey
Sign Up to like & getrecommendations! Published in 2023 at "Pediatric Transplantation"
DOI: 10.1111/petr.14464
Abstract: Maple syrup urine disease (MSUD) is an autosomal recessive inherited disorder. Despite the advances in medical nutrition therapies, classical phenotype causes severe neurological disorders and sudden death. It is known that MSUD patients do not… read more here.
Keywords: long term; maple syrup; syrup urine; transplantation ... See more keywords
Teaching NeuroImage: Optic Pathway Involvement in Maple Syrup Urine Disease
Sign Up to like & getrecommendations! Published in 2022 at "Neurology"
DOI: 10.1212/wnl.0000000000201290
Abstract: A 10-day-old neonate presented with vomiting and irritability. Diffusion-weighted imaging showed abnormal signal intensities, including characteristic involvement of the optic pathway (Figure, A and B). Maple syrup urine disease (MSUD) was suspected. Blood tests confirmed… read more here.
Keywords: maple syrup; optic pathway; involvement; syrup urine ... See more keywords
Outcomes from a Single Transplant Center of 5 Pediatric Cases of Domino Liver Transplantation from Live Donors with Maple Syrup Urine Disease.
Sign Up to like & getrecommendations! Published in 2023 at "Annals of transplantation"
DOI: 10.12659/aot.939893
Abstract: Background Maple syrup urine disease (MSUD) is a rare genetic deficiency of the branched-chain α-keto acid dehydrogenase (BCKAD) complex that breaks down amino acids, resulting in multi-organ failure. This report is of 5 pediatric cases… read more here.
Keywords: maple syrup; disease; center; transplantation ... See more keywords
Identification of gene mutations in six Chinese patients with maple syrup urine disease
Sign Up to like & getrecommendations! Published in 2023 at "Frontiers in Genetics"
DOI: 10.3389/fgene.2023.1132364
Abstract: Background: Maple syrup urine disease (MSUD) is a rare autosomal recessive amino acid metabolic disease. This study is to identify the pathogenic genetic factors of six cases of MUSD and evaluates the application value of… read more here.
Keywords: maple syrup; disease; syrup urine; high throughput ... See more keywords
A Smart Monitoring System for Self-Nutrition Management in Pediatric Patients with Inherited Metabolic Disorders: Maple Syrup Urine Disease (MSUD)
Sign Up to like & getrecommendations! Published in 2023 at "Healthcare"
DOI: 10.3390/healthcare11020178
Abstract: A metabolic disorder is due to a gene mutation that causes an enzyme deficiency which leads to metabolism problems. Maple Syrup Urine Disease (MSUD) is one of the most common and severe hereditary metabolic disorders… read more here.
Keywords: system; maple syrup; food; syrup urine ... See more keywords
Knowledge-Based Dietary Intake Recommendations of Nutrients for Pediatric Patients with Maple Syrup Urine Disease
Sign Up to like & getrecommendations! Published in 2023 at "Healthcare"
DOI: 10.3390/healthcare11030301
Abstract: Maple syrup urine disease (MSUD) is a metabolic disorder characterized by a difficulty to digest and process proteins necessary for growth. To monitor and maintain the ideal growth of children with MSUD, caregivers need to… read more here.
Keywords: maple syrup; tool; msud; syrup urine ... See more keywords