Association of rs3750920 polymorphism in TOLLIP with clinical characteristics of fibrosing interstitial lung diseases in Japanese
Sign Up to like & getrecommendations! Published in 2021 at "Scientific Reports"
DOI: 10.1038/s41598-021-95869-9
Abstract: TOLLIP polymorphism has been implicated in the development and prognosis of idiopathic pulmonary fibrosis (IPF), mainly in whites. However, ethnic differences in the characteristics of other interstitial pneumonia (non-IPF) subtypes are unclear. We evaluated the… read more here.
Keywords: fibrosing interstitial; association rs3750920; non ipf; clinical characteristics ... See more keywords
Progressive fibrosing interstitial lung diseases: current practice in diagnosis and management
Sign Up to like & getrecommendations! Published in 2019 at "Current Medical Research and Opinion"
DOI: 10.1080/03007995.2019.1647040
Abstract: Abstract Objective: Some patients with interstitial lung diseases (ILDs) other than idiopathic pulmonary fibrosis (IPF) develop a progressive fibrosing phenotype. We investigated the diagnosis and management of non-IPF ILDs using data from a survey of… read more here.
Keywords: diagnosis; non ipf; interstitial lung; lung diseases ... See more keywords
Central lung gene expression associates with myofibroblast features in idiopathic pulmonary fibrosis
Sign Up to like & getrecommendations! Published in 2023 at "BMJ Open Respiratory Research"
DOI: 10.1136/bmjresp-2022-001391
Abstract: Rationale Contribution of central lung tissues to pathogenesis of idiopathic pulmonary fibrosis (IPF) remains unknown. Objective To ascertain the relationship between cell types of IPF-central and IPF-peripheral lung explants using RNA sequencing (RNA-seq) transcriptome. Methods… read more here.
Keywords: non ipf; ipf; idiopathic pulmonary; central ipf ... See more keywords
Real-world impact of antifibrotics on prognosis in patients with progressive fibrosing interstitial lung disease
Sign Up to like & getrecommendations! Published in 2023 at "RMD Open"
DOI: 10.1136/rmdopen-2022-002667
Abstract: Objective No studies have demonstrated the real-world efficacy of antifibrotics for progressive fibrosing interstitial lung disease (PF-ILD). Therefore, we evaluated the efficacy of antifibrotics in patients with PF-ILD. Methods We retrospectively reviewed the medical records… read more here.
Keywords: non ipf; ipf; real world; progressive fibrosing ... See more keywords
Health care resources utilisation and costs in patients with non-IPF progressive fibrosing interstitial lung disease
Sign Up to like & getrecommendations! Published in 2018 at "European Respiratory Journal"
DOI: 10.1183/13993003.congress-2018.pa3658
Abstract: Background: Idiopathic pulmonary fibrosis (IPF) is the classic fibrosing interstitial lung disease (ILD), but it accounts for Aims and objectives: To assess healthcare resource use and cost in non-IPF PF-ILD. Methods: We analysed US-based medical… read more here.
Keywords: fibrosing interstitial; patients non; non ipf; lung disease ... See more keywords
Antifibrotic therapy for fibrotic lung disease beyond idiopathic pulmonary fibrosis
Sign Up to like & getrecommendations! Published in 2019 at "European Respiratory Review"
DOI: 10.1183/16000617.0022-2019
Abstract: Two antifibrotic medications (nintedanib and pirfenidone) were recommended (conditionally) for the treatment of patients with idiopathic pulmonary fibrosis (IPF) in the 2015 IPF evidence-based guidelines. These medications have been shown to reduce the rate of… read more here.
Keywords: fibrotic lung; idiopathic pulmonary; non ipf; disease ... See more keywords
Claims-based Prevalence of Disease Progression among Patients with Non-IPF Fibrosing Interstitial Lung Disease in the US.
Sign Up to like & getrecommendations! Published in 2022 at "Annals of the American Thoracic Society"
DOI: 10.1513/annalsats.202102-222oc
Abstract: RATIONALE Chronic fibrosing interstitial lung disease (ILD) with a progressive phenotype is a clinical concept describing the broad group of interstitial lung diseases characterized by progressive pulmonary fibrosis. The prevalence of progressive fibrotic ILDs other… read more here.
Keywords: non ipf; disease; prevalence; progression ... See more keywords
Serum Progranulin Level Might Differentiate Non-IPF ILD from IPF
Sign Up to like & getrecommendations! Published in 2023 at "International Journal of Molecular Sciences"
DOI: 10.3390/ijms24119178
Abstract: Diagnosing interstitial lung disease (ILD) can be a challenging process. New biomarkers may support diagnostic decisions. Elevated serum progranulin (PGRN) levels have been reported in liver fibrosis and dermatomyositis-associated acute interstitial pneumonia. Our aim was… read more here.
Keywords: non ipf; ipf; pgrn; level ... See more keywords
Decreased Survival and Lung Function in Progressive Pulmonary Fibrosis
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DOI: 10.3390/medicina59020296
Abstract: Background and Objectives: Progressive pulmonary fibrosis (PPF) is a recently described term reserved for patients with fibrotic ILD other than idiopathic pulmonary fibrosis (IPF) with fast clinical deterioration. Here, survival and prognostic biomarkers at the… read more here.
Keywords: non ipf; survival; pulmonary fibrosis; ppf ... See more keywords