Non-lupus full-house nephropathy—immune dysregulation as a rare cause of pediatric nephrotic syndrome: Questions
Sign Up to like & getrecommendations! Published in 2021 at "Pediatric Nephrology"
DOI: 10.1007/s00467-021-05359-3
Abstract: We present the case of a boy, who was first referred to our nephrology department in 2013 at the age of 6 with periorbital oedema, nephrotic range of proteinuria (100 mg/m2/h), glomerular haematuria, hypalbuminaemia and… read more here.
Keywords: full house; nephrotic syndrome; nephrology; non lupus ... See more keywords
Non-lupus full-house nephropathy—immune dysregulation as a rare cause of pediatric nephrotic syndrome: Answers
Sign Up to like & getrecommendations! Published in 2021 at "Pediatric Nephrology"
DOI: 10.1007/s00467-021-05378-0
Abstract: Based on the synchroneity of severe infections, multiple autoimmune disorders, atopic dermatitis, chronic diarrhoea and insufficient weight gain, the “immunodysregulation, polyendocrinopathy, enteropathy, X-linked” (IPEX) or IPEXlike syndrome was first suspected at the age of 8… read more here.
Keywords: syndrome; lupus full; treg; full house ... See more keywords
Non-lupus full house nephropathy in pediatrics: Case reports
Sign Up to like & getrecommendations! Published in 2020 at "Biomedica : revista del Instituto Nacional de Salud"
DOI: 10.7705/biomedica.4863
Abstract: Full house nephropathy is defined as the simultaneous detection of IgA, IgG, IgM, C3, and C1q deposits by immunofluorescence, usually indicating lupus nephritis. There are patients with this immunofluorescence pattern, but with negative autoantibody serology,… read more here.
Keywords: house nephropathy; lupus full; serology; non lupus ... See more keywords