Achievement of the longest survival of paraneoplastic pemphigus with bronchiolitis obliterans associated with follicular lymphoma using R-CHOP chemotherapy
Sign Up to like & getrecommendations! Published in 2017 at "International Journal of Hematology"
DOI: 10.1007/s12185-017-2305-2
Abstract: Paraneoplastic pemphigus (PNP) is a rare, fatal, paraneoplastic autoimmune mucocutaneous blistering disease, commonly associated with lymphoproliferative disorders, including malignant lymphomas. Lymphoproliferative disorders associated with PNP are sometimes associated with a serious lung complication, bronchiolitis obliterans… read more here.
Keywords: lymphoma; bronchiolitis obliterans; pnp; follicular lymphoma ... See more keywords
Successful treatment of paraneoplastic pemphigus and bronchiolitis obliterans associated with follicular lymphoma with obinutuzumab and bendamustine.
Sign Up to like & getrecommendations! Published in 2021 at "Current problems in cancer"
DOI: 10.1016/j.currproblcancer.2021.100813
Abstract: We herein report the rare case of a 72-year-old female who presented with paraneoplastic pemphigus (PNP) and bronchiolitis obliterans (BO) associated with follicular lymphoma (FL), who was successfully treated with obinutuzumab (GA101; G) and bendamustine… read more here.
Keywords: obliterans associated; follicular lymphoma; paraneoplastic pemphigus; associated follicular ... See more keywords
Buccal paraneoplastic pemphigus multi-resistant: Case report and review of diagnostic and therapeutic strategies.
Sign Up to like & getrecommendations! Published in 2018 at "Journal of stomatology, oral and maxillofacial surgery"
DOI: 10.1016/j.jormas.2018.06.003
Abstract: Paraneoplastic pemphigus is a rare autoimmune blistering disease generally associated with malignancy. The clinical presentation consists typically of painful and diffuse erosive stomatitis that may be accompanied by polymorphic skin lesions and systemic involvement. Diagnosis… read more here.
Keywords: buccal paraneoplastic; case; report; pemphigus multi ... See more keywords
Ocular Onset of Paraneoplastic Pemphigus Presenting as Hyperemic Conjunctivitis and Massive Bilateral Eyelid Ulceration: A Case Report and Literature Review
Sign Up to like & getrecommendations! Published in 2018 at "Ocular Immunology and Inflammation"
DOI: 10.1080/09273948.2016.1203958
Abstract: ABSTRACT Introduction: Paraneoplastic clinical signs are characterized by a large and heterogeneous variety of manifestations due to several possible underlying neoplasms. Paraneoplastic pemphigus (PNP) is a particular paraneoplastic variety that usually primarily affects the dermic… read more here.
Keywords: hyperemic conjunctivitis; eyelid ulceration; paraneoplastic pemphigus; report ... See more keywords
Paraneoplastic pemphigus with anti‐BP180 autoantibodies and Castleman disease
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DOI: 10.1111/bjd.14877
Abstract: Paraneoplastic pemphigus (PNP) is commonly associated with IgG-autoantibodies against desmoglein 1 and 3, plakins (desmoplakin I and II, envoplakin, periplakin), desmocollins 1-3, BP2301 and α2-macroglobulin-like-1 (A2ML1)2. The major autoantigen of bullous pemphigoid (BP), pemphigoid gestationis… read more here.
Keywords: pemphigus anti; bp180 autoantibodies; anti bp180; autoantibodies castleman ... See more keywords
Paraneoplastic pemphigus: Revised diagnostic criteria based on literature analysis
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Cutaneous Pathology"
DOI: 10.1111/cup.14004
Abstract: Paraneoplastic pemphigus (PNP) is a rare autoimmune bullous disease classically associated with an underlying neoplasm. The heterogeneous clinical and histopathologic features of the disease make diagnosis challenging for clinicians. There are no formally accepted diagnostic… read more here.
Keywords: criteria based; pemphigus revised; revised diagnostic; diagnostic criteria ... See more keywords
Paraneoplastic pemphigus without mucosal lesions in a patient with ovarian cancer
Sign Up to like & getrecommendations! Published in 2021 at "International Journal of Dermatology"
DOI: 10.1111/ijd.15667
Abstract: Paraneoplastic pemphigus without mucosal lesions in a patient with ovarian cancer Dear Editor, A 48-year-old female with a BRCA2 gene mutation and a family history of breast cancer presented with a 6-month history of widespread… read more here.
Keywords: paraneoplastic pemphigus; cancer; pemphigus; without mucosal ... See more keywords
Postpartum Castleman disease presenting as paraneoplastic pemphigus: a case report
Sign Up to like & getrecommendations! Published in 2022 at "International Journal of Dermatology"
DOI: 10.1111/ijd.16505
Abstract: References 1 As kın € O, Engin B, Gencebay G, T€ uz€ un Y. A multistep approach to the diagnosis of rare genodermatoses. Clin Dermatol. 2020;38:399–407. 2 Chiu FP-C, Doolan BJ, McGrath JA, Onoufriadis A.… read more here.
Keywords: pemphigus case; paraneoplastic pemphigus; castleman disease; disease presenting ... See more keywords
Paraneoplastic autoimmune multiorgan syndrome (paraneoplastic pemphigus): How and why should we recognize atypical cases early?
Sign Up to like & getrecommendations! Published in 2022 at "Journal of the European Academy of Dermatology and Venereology"
DOI: 10.1111/jdv.18724
Abstract: Paraneoplastic autoimmune multiorgan syndrome (PAMS), originally described by Anhalt et al.1 in 1990 as paraneoplastic pemphigus, is a rare and often fatal autoimmune bullous disease of the skin and mucous membranes, almost always associated with… read more here.
Keywords: autoimmune multiorgan; multiorgan syndrome; diagnosis; paraneoplastic autoimmune ... See more keywords
Paraneoplastic pemphigus associated with Castleman's disease
Sign Up to like & getrecommendations! Published in 2023 at "Journal of Paediatrics and Child Health"
DOI: 10.1111/jpc.16361
Abstract: A 15-year-old male, with personal history of limb-girdle muscular dystrophy, was admitted to the paediatric ward for a 1-month history of pruritic, generalised, polymorphous eruption and severe painful mucositis. Two months earlier he had been… read more here.
Keywords: improvement; day; mucositis; disease ... See more keywords
Paraneoplastic pemphigus associated with Castleman disease: A multicenter case series
Sign Up to like & getrecommendations! Published in 2022 at "Pediatric Dermatology"
DOI: 10.1111/pde.15138
Abstract: Paraneoplastic pemphigus (PNP) is a rare, often fatal, autoimmune blistering disease of the skin and mucous membranes. In children, PNP is frequently associated with Castleman disease (CD). This series describes five cases of PNP associated… read more here.
Keywords: series; disease; paraneoplastic pemphigus; castleman disease ... See more keywords