Acneiform Eruption Following Elexacaftor-Tezacaftor-Ivacaftor Treatment in Patients With Cystic Fibrosis.
Sign Up to like & getrecommendations! Published in 2022 at "JAMA dermatology"
DOI: 10.1001/jamadermatol.2022.5208
Abstract: Importance A new treatment for cystic fibrosis combining 3 CFTR modulators-elexacaftor (ELX), tezacaftor (TEZ), and ivacaftor (IVA)-has recently been approved for cystic fibrosis treatment. The cutaneous adverse effects following treatment with this combination are poorly… read more here.
Keywords: cystic fibrosis; patients cystic; iva; treatment ... See more keywords
Association of Body Mass Index With Clinical Outcomes in Patients With Cystic Fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "JAMA Network Open"
DOI: 10.1001/jamanetworkopen.2022.0740
Abstract: Key Points Question Is higher-than-normal body mass index (BMI) associated with better clinical outcomes in patients with cystic fibrosis? Findings In this systematic review and meta-analysis of studies including 9114 patients with cystic fibrosis, BMI… read more here.
Keywords: clinical outcomes; patients cystic; body mass; mass index ... See more keywords
Improvements in anthropometric measures and gastrointestinal tolerance in patients with cystic fibrosis by using a digestive enzyme cartridge with overnight enteral nutrition
Sign Up to like & getrecommendations! Published in 2022 at "Nutrition in Clinical Practice"
DOI: 10.1002/ncp.10831
Abstract: Abstract Background Patients with cystic fibrosis (CF) and pancreatic insufficiency are at risk for suboptimal fat absorption, inability to maintain weight, poor growth, and increased gastrointestinal (GI) symptoms due to malabsorption. Enteral nutrition (EN) is… read more here.
Keywords: patients cystic; cartridge; using digestive; enzyme cartridge ... See more keywords
Outcome evaluation of a pharmacy‐based therapy management program for patients with cystic fibrosis
Sign Up to like & getrecommendations! Published in 2018 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.23978
Abstract: To compare medication adherence, pulmonary exacerbations, healthcare utilization, and costs for patients with cystic fibrosis (CF) who utilized a pharmacy‐based therapy management program to a matched control group. We hypothesized that patient management services would… read more here.
Keywords: cystic fibrosis; therapy management; management; patients cystic ... See more keywords
Cystic fibrosis‐related liver disease is an independent risk factor for mortality and increased health care resource utilization in hospitalized pediatric patients with cystic fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.25941
Abstract: Cystic fibrosis‐related liver disease (CFLD) is more prevalent in recent decades due to the increasing life expectancy of patients with cystic fibrosis (CF). There is paucity of population‐level data on the impact of CFLD on… read more here.
Keywords: patients cystic; fibrosis related; related liver; liver disease ... See more keywords
Retrospective review of vancomycin monitoring via trough only versus two‐point estimated area under the curve in pediatric and adult patients with cystic fibrosis
Sign Up to like & getrecommendations! Published in 2022 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.26190
Abstract: The primary objective of this study was to compare the occurrence of acute kidney injury (AKI) in patients with cystic fibrosis (CF) receiving intravenous (IV) vancomycin monitored through single serum trough concentrations and two‐point estimated… read more here.
Keywords: estimated area; patients cystic; two point; point estimated ... See more keywords
Outcome of elexacaftor/tezacaftor/ivacaftor therapy in patients with cystic fibrosis and solid organ transplantation
Sign Up to like & getrecommendations! Published in 2022 at "Pediatric Pulmonology"
DOI: 10.1002/ppul.26217
Abstract: We report a case series of four patients with cystic fibrosis (CF) and previous solid organ transplantation (SOT) receiving elexacaftor/tezacaftor/ivacaftor therapy for 6 months or more. Data was collected retrospectively. The treatment was well tolerated… read more here.
Keywords: organ transplantation; patients cystic; elexacaftor tezacaftor; tezacaftor ivacaftor ... See more keywords
Exercise testing in patients with cystic fibrosis—importance of ventilatory parameters
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DOI: 10.1007/s00421-018-4018-5
Abstract: BackgroundVentilatory parameters obtained during exercise predict survival in several chronic diseases; however, long-term changes in exercise ventilatory parameters in patients with cystic fibrosis (CF) have yet to be examined and potential differences between sexes in… read more here.
Keywords: exercise ventilatory; patients cystic; vo2 peak; ventilatory ... See more keywords
Respiratory physical therapy techniques recommended for patients with cystic fibrosis treated in specialized centers.
Sign Up to like & getrecommendations! Published in 2019 at "Brazilian journal of physical therapy"
DOI: 10.1016/j.bjpt.2019.11.003
Abstract: BACKGROUND Respiratory therapy is a part of the treatment of patients with cystic fibrosis (CF). However, there is no information about the main factors influencing the recommendation of the use of different techniques or devices… read more here.
Keywords: cystic fibrosis; treatment; therapy techniques; patients cystic ... See more keywords
Heterogeneity in Survival in Adult Patients With Cystic Fibrosis With FEV1 < 30% of Predicted in the United States
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DOI: 10.1016/j.chest.2017.01.019
Abstract: BACKGROUND: Lung transplantation (LTx) is frequently considered for patients with cystic fibrosis (CF) when the FEV1 reaches < 30%. This study estimated transplant‐free survival for patients with CF and an FEV1 < 30% and identified… read more here.
Keywords: fibrosis fev1; cystic fibrosis; patients cystic; fev1 ... See more keywords
Applying recent advances in the science of CFTR-based therapeutics to improve outcomes in patients with cystic fibrosis
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Cystic Fibrosis"
DOI: 10.1016/j.jcf.2017.03.002
Abstract: Abstract The content for this activity is based on the satellite symposium, “Applying Recent Advances in the Science of CFTR-based Therapeutics to Improve Outcomes in Patients With Cystic Fibrosis”, that was presented at the 30th… read more here.
Keywords: cystic fibrosis; fibrosis; based therapeutics; cftr based ... See more keywords