Anesthesia for Complex Cardiovascular Surgery in a Patient With PHACES Syndrome and Review of the Literature.
Sign Up to like & getrecommendations! Published in 2017 at "Journal of cardiothoracic and vascular anesthesia"
DOI: 10.1053/j.jvca.2016.07.010
Abstract: NFANTILE HEMANGIOMAS ARE a common benign vascular tumor occurring in 5% to 10% of infants 1 and resolve without complication or medical intervention. A subgroup of patients with hemangiomas have associated structural anomalies causing significant… read more here.
Keywords: anesthesia complex; phaces syndrome; complex cardiovascular; hemangiomas ... See more keywords
PHACES syndrome with ectopia cordis and hemihypertrophy
Sign Up to like & getrecommendations! Published in 2019 at "Baylor University Medical Center Proceedings"
DOI: 10.1080/08998280.2018.1548263
Abstract: Abstract PHACES is the acronym describing the phenotypic association of posterior fossa anomalies, facial hemangioma, cardiac and eye anomalies, and sternal defects. To date, more than 300 cases of PHACE(S) have been reported. We present… read more here.
Keywords: ectopia cordis; syndrome ectopia; hemihypertrophy; cordis hemihypertrophy ... See more keywords
Asymmetric Meckel Cave Enlargement: A Potential Marker of PHACES Syndrome
Sign Up to like & getrecommendations! Published in 2017 at "American Journal of Neuroradiology"
DOI: 10.3174/ajnr.a5140
Abstract: BACKGROUND AND PURPOSE: PHACES syndrome is a complex of morphologic abnormalities of unknown cause and includes posterior fossa abnormalities; head and neck infantile hemangiomas; arterial, cardiac, and eye anomalies; and sternal or abdominal wall defects.… read more here.
Keywords: meckel cave; asymmetric meckel; enlargement potential; cave enlargement ... See more keywords
Corkscrew aortic arch in PHACES syndrome: Multimodal imaging of an unusual morphology of tortuous aortic arch in a rare but well-defined syndrome
Sign Up to like & getrecommendations! Published in 2019 at "Annals of Pediatric Cardiology"
DOI: 10.4103/apc.apc_188_18
Abstract: PHACES syndrome, a diffuse aortocraniocerebral vasculopathy, is a neural tube migration disorder, characterized by aortic coarctation and aberrant arch branches. Clinical diagnosis, echocardiography, and surgical management of coarctation in this syndrome are challenging due to… read more here.
Keywords: phaces syndrome; multimodal imaging; aortic arch; arch ... See more keywords