Impact of body composition and genotype on haemodynamics during surgery for pheochromocytoma and paraganglioma
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Cachexia, Sarcopenia and Muscle"
DOI: 10.1002/jcsm.13071
Abstract: Maintaining intraoperative haemodynamic stability can reduce cardiovascular complications during surgery for pheochromocytoma and paraganglioma (PPGL). Risk factors such as tumour size and catecholamine levels are reported to predict haemodynamic responses during surgery for PPGL. We… read more here.
Keywords: pheochromocytoma paraganglioma; surgery pheochromocytoma; body composition;
Correlation between catecholamines and echocardiographic parameters in patients with pheochromocytoma and paraganglioma
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Clinical Ultrasound"
DOI: 10.1002/jcu.23290
Abstract: To analyze the correlation between catecholamines and echocardiographic parameters in patients with pheochromocytoma and paraganglioma (PPGL). read more here.
Keywords: pheochromocytoma paraganglioma; correlation catecholamines; patients pheochromocytoma; echocardiographic parameters ... See more keywords
Genetic testing for pheochromocytoma and paraganglioma: SDHx carriers’ experiences
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Genetic Counseling"
DOI: 10.1002/jgc4.1390
Abstract: Pheochromocytoma and paraganglioma are frequently hereditary tumors commonly associated with succinate dehydrogenase (SDHx) pathogenic variants (PV). Genetic testing is recommended to relatives of patients carrying SDHx PV. This study aims to explore the experiences associated… read more here.
Keywords: sdhx; testing pheochromocytoma; genetic testing; pheochromocytoma paraganglioma ... See more keywords
Pheochromocytoma and Paraganglioma in Pregnancy: a New Era
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DOI: 10.1007/s11886-021-01485-4
Abstract: Pheochromocytoma and paraganglioma (PPGL) in pregnancy is a rare entity and management of these patients is fraught with uncertainty. Our objective is to review current literature and discuss diagnosis and management of these patients. Outcomes… read more here.
Keywords: pregnancy; ppgl pregnancy; pregnancy new; paraganglioma pregnancy ... See more keywords
Re-operative Surgery for Pheochromocytoma-Paraganglioma: Analysis of 13 Cases from a Single Institution
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DOI: 10.1007/s12262-017-1658-3
Abstract: Re-operative adrenal surgery for recurrent pheochromocytoma/paraganglioma (PCC/PGL) is a therapeutic situation not commonly encountered. The recurrence rate of pheochromocytoma is estimated to be 6.1–16.5% of patients from published retrospective series; there are no reports from… read more here.
Keywords: surgery; operative surgery; pheochromocytoma; analysis ... See more keywords
Recent Advances in Radiopharmaceutical Theranostics of Pheochromocytoma and Paraganglioma.
Sign Up to like & getrecommendations! Published in 2023 at "Seminars in nuclear medicine"
DOI: 10.1053/j.semnuclmed.2022.12.005
Abstract: As a rare kind of non-epithelial neuroendocrine neoplasms, paragangliomas (PGLs) exhibit various clinical characteristics with excessive catecholamine secretion and have been a research focus in recent years. Although several modalities are available nowadays, radiopharmaceuticals play… read more here.
Keywords: theranostics pheochromocytoma; pheochromocytoma paraganglioma; advances radiopharmaceutical; mibg ... See more keywords
Functional Imaging Evidence of Tumor Response to High-Specific-Activity 131I-MIBG Therapy in an 84-Year-Old Patient With Metastatic Pheochromocytoma/Paraganglioma.
Sign Up to like & getrecommendations! Published in 2023 at "Clinical nuclear medicine"
DOI: 10.1097/rlu.0000000000004519
Abstract: ABSTRACT An 84-year-old man with history of metastatic pheochromocytoma/paraganglioma (mPPGL) received surgery 13 years ago, with recent biopsy-proven mPPGL in the T11. 123I-MIBG scan showed MIBG-avid liver and osseous. Given his medical condition and body… read more here.
Keywords: pheochromocytoma paraganglioma; metastatic pheochromocytoma; year old; patient ... See more keywords
Fumarate hydratase gene germline variants and mosaicism associated with pheochromocytoma and paraganglioma
Sign Up to like & getrecommendations! Published in 2022 at "Annals of the New York Academy of Sciences"
DOI: 10.1111/nyas.14866
Abstract: Fumarate hydratase (FH) catalyzes the conversion of fumaric acid to L‐malic acid. Heterozygous variants of the human fumarate hydratase gene (FH) predispose to hereditary leiomyomatosis and renal cell cancer and, rarely, pheochromocytoma/paraganglioma (PPGL). No mosaic… read more here.
Keywords: pheochromocytoma paraganglioma; germline variants; fumarate hydratase; hydratase gene ... See more keywords
Circulating GLP-1 Levels in Patients with Pheochromocytoma/Paraganglioma
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DOI: 10.1155/2022/4203018
Abstract: The sympathoadrenal system has been shown to stimulate the secretory activity of enteroendocrine cells, although the response is transient. Our aim was to investigate the effects of long-term catecholamine excess on circulating glucagon-likepeptide-1 (GLP-1) levels… read more here.
Keywords: glp; pheochromocytoma paraganglioma; circulating glp; patients pheochromocytoma ... See more keywords
Establishment of reference intervals for plasma metanephrines in seated position measured by LC-MS/MS and assessment of diagnostic performance in pheochromocytoma/paraganglioma
Sign Up to like & getrecommendations! Published in 2023 at "Annals of Clinical Biochemistry"
DOI: 10.1177/00045632231154731
Abstract: Background The use of supine reference intervals instead of the corresponding seated reference intervals for seated plasma-free metanephrines (MNs) in pheochromocytoma/paraganglioma (PPGL) screening has been controversial in recent years. Each clinical laboratory should choose the… read more here.
Keywords: pheochromocytoma paraganglioma; reference; seated plasma; diagnostic performance ... See more keywords
Intraoperative hypotension is associated with increased postoperative complications in patients undergoing surgery for pheochromocytoma-paraganglioma: a retrospective cohort study
Sign Up to like & getrecommendations! Published in 2020 at "BMC Anesthesiology"
DOI: 10.1186/s12871-020-01066-y
Abstract: Background Dramatic hemodynamic fluctuation occurs frequently during surgery for pheochromocytoma or paraganglioma. However, the criteria of intraoperative hemodynamic instability vary widely, and most of them were defined arbitrarily but not according to patients’ prognosis. The… read more here.
Keywords: surgery; postoperative complications; surgery pheochromocytoma; pheochromocytoma paraganglioma ... See more keywords