Pleuroparenchymal fibroelastosis-like lesions in patients with interstitial pneumonia diagnosed by multidisciplinary discussion with surgical lung biopsy
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DOI: 10.1016/j.ejro.2020.100298
Abstract: Purpose The present study aimed to evaluate the significance of Pleuroparenchymal fibroelastosis (PPFE)-like lesions in predicting prognosis in patients with chronic interstitial pneumonia (IP). Method The present study enrolled 207 patients with IP in whom… read more here.
Keywords: pleuroparenchymal fibroelastosis; like lesions; ppfe like; surgical lung ... See more keywords
Pleuroparenchymal fibroelastosis diagnosed by multidisciplinary discussions in Japan.
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DOI: 10.1016/j.rmed.2018.06.022
Abstract: BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) is a rare subset of idiopathic interstitial pneumonias. No large-scale clinical studies of PPFE have been published. The aim of the study was to clarify the clinical and physiological characteristics of… read more here.
Keywords: multidisciplinary discussions; pleuroparenchymal fibroelastosis; fibroelastosis diagnosed; diagnosed multidisciplinary ... See more keywords
Prognostic role of KL‐6 in SSc‐ILD patients with pleuroparenchymal fibroelastosis
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DOI: 10.1111/eci.13543
Abstract: Krebs von den Lungen‐6 (KL‐6) is a high‐molecular‐weight (200kDa) glycoprotein proposed as a diagnostic biomarker for differentiating interstitial lung disease (ILD). Systemic sclerosis (SSc) is a rare immune‐mediated disorder, and ILD is the leading cause… read more here.
Keywords: role ssc; pleuroparenchymal fibroelastosis; ssc ild; ild patients ... See more keywords
Pleuroparenchymal fibroelastosis associated with telomerase reverse transcriptase mutations
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DOI: 10.1183/13993003.02022-2016
Abstract: We read with great interest the article by Newton et al. [1]. They found that mutations in the telomere maintenance machinery genes (telomerase reverse transcriptase (TERT), telomerase RNA component (TERC), regulator of telomere elongation helicase… read more here.
Keywords: reverse transcriptase; telomerase reverse; fibroelastosis associated; pleuroparenchymal fibroelastosis ... See more keywords
Lung involvement during the prediagnostic phase of idiopathic pleuroparenchymal fibroelastosis
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DOI: 10.1183/23120541.00548-2021
Abstract: Idiopathic pleuroparenchymal fibroelastosis (IPPFE) is a rare interstitial pneumonia that predominantly affects the upper lung fields [1, 2]. A pulmonary apical cap (PAC) is an imaging finding resembling that for PPFE that does not show… read more here.
Keywords: lung involvement; pleuroparenchymal fibroelastosis; lung; phase ... See more keywords
Delineating associations of progressive pleuroparenchymal fibroelastosis in patients with pulmonary fibrosis
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DOI: 10.1183/23120541.00637-2022
Abstract: Background Computer quantification of baseline computed tomography (CT) radiological pleuroparenchymal fibroelastosis (PPFE) associates with mortality in idiopathic pulmonary fibrosis (IPF). We examined mortality associations of longitudinal change in computer-quantified PPFE-like lesions in IPF and fibrotic… read more here.
Keywords: ppfe; ppfe like; like lesions; pleuroparenchymal fibroelastosis ... See more keywords
Unilateral pleuroparenchymal fibroelastosis as a rare form of idiopathic interstitial pneumonia: A case report
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DOI: 10.12998/wjcc.v8.i18.4186
Abstract: BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia characterized by predominantly upper lobe involvement with pleural fibrosis and subjacent parenchymal fibrosis. Recently, there have been increasing reports of PPFE, and PPFE might coexist… read more here.
Keywords: pleuroparenchymal fibroelastosis; idiopathic interstitial; lobe; ppfe ... See more keywords
Pleuroparenchymal Fibroelastosis with a Predominantly Airway-centered Distribution: A Late Complication of Chemotherapy
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DOI: 10.2169/internalmedicine.7402-21
Abstract: Airway-centered fibroelastosis is a distinct entity characterized by prominent airway-centered elastosis of the upper lobe with little or no pleural involvement. Little is known regarding its etiology; however, it was reported to have an idiopathic… read more here.
Keywords: fibroelastosis predominantly; pleuroparenchymal fibroelastosis; predominantly airway; airway centered ... See more keywords
Lung Transplantation for Pleuroparenchymal Fibroelastosis: A Single-Center Experience with Revision of Literature
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DOI: 10.3390/biomedicines11061505
Abstract: Pleuroparenchymal fibroelastosis (PPFE) is a rare condition characterized by fibrosis involving the pleura and the upper lobes which can be idiopathic or secondary to chemotherapy, transplantations and occupational exposure. For the end-stage form, lung transplantation… read more here.
Keywords: lung transplantation; pleuroparenchymal fibroelastosis; center;
Pleuroparenchymal Fibroelastosis-like Lesions in Clinical Practice: A Rare Entity? Review of a Radiological Database
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DOI: 10.3390/diagnostics13091627
Abstract: Background: Pleuroparenchymal Fibroelastosis (PPFE) is a rare disease that consists of elastofibrosis that involves the pleura and subpleural lung parenchyma; it is an unusual pulmonary disease with unique clinical, radiological and pathological characteristics. According to… read more here.
Keywords: ppfe; disease; like lesions; pleuroparenchymal fibroelastosis ... See more keywords