Can Computed Tomography Scans Reliably Distinguish Pleuropulmonary Blastoma From Congenital Lung Malformations?
Sign Up to like & getrecommendations! Published in 2022 at "JAMA network open"
DOI: 10.1001/jamanetworkopen.2022.19826
Abstract: The differentiation between congenital lung malformations (CLMs) and pleuropulmonary blastoma (PPB) is a diagnostic conundrum with potentially life-altering consequences. Congenital lung malformations are a group of diagnoses that include benign congenital pulmonary airway malformations (CPAMs),… read more here.
Keywords: congenital lung; pleuropulmonary blastoma; lung malformations; type ... See more keywords
Type I and Ir pleuropulmonary blastoma (PPB): A report from the International PPB/DICER1 Registry
Sign Up to like & getrecommendations! Published in 2022 at "Cancer"
DOI: 10.1002/cncr.34593
Abstract: Pleuropulmonary blastoma (PPB) is the most common lung cancer of infancy and early childhood. Type I PPB is a purely cystic lesion that has a microscopic population of primitive small cells with or without rhabdomyoblastic… read more here.
Keywords: blastoma ppb; ppb; type; type pleuropulmonary ... See more keywords
Fine needle aspiration in intraocular metastasis from pleuropulmonary blastoma. A case report and a review of the literature
Sign Up to like & getrecommendations! Published in 2017 at "Diagnostic Cytopathology"
DOI: 10.1002/dc.23618
Abstract: Pleuropulmonary blastoma (PPB) is a rare primitive intrathoracic malignant neoplasm that occurs almost exclusively in children and adolescents. PPB is classified into three types according to the presence of cystic and solid areas. We report… read more here.
Keywords: pleuropulmonary blastoma; needle aspiration; metastasis; fine needle ... See more keywords
Pleuropulmonary blastoma (PPB) with central nervous system metastasis: case report, imaging findings, and review of literature
Sign Up to like & getrecommendations! Published in 2024 at "Acta Chirurgica Belgica"
DOI: 10.1080/00015458.2024.2365503
Abstract: Abstract Pleuropulmonary blastoma (PPB) is a very rare tumor of the chest seen predominantly in young children with great heterogeneity and clinical, biochemical, and biological complexity and recognized, described, and classified as distinct from the… read more here.
Keywords: pleuropulmonary blastoma; central nervous; ppb; blastoma ... See more keywords
Pleuropulmonary blastoma: Difficulty in diagnosis and treatment of a case in Vietnam
Sign Up to like & getrecommendations! Published in 2020 at "Pediatric Hematology and Oncology"
DOI: 10.1080/08880018.2020.1818905
Abstract: Abstract Pleuropulmonary blastoma (PPB) is a rare malignant tumor in childhood cancer. This type of tumor is difficult to identify and can easily be misdiagnosed. The International PPB protocol is a complicated and aggressive protocol.… read more here.
Keywords: vietnam; pleuropulmonary blastoma; treatment; case ... See more keywords
Pleuropulmonary Blastoma: A Single-center Case Series of 6 Patients
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Pediatric Hematology/Oncology"
DOI: 10.1097/mph.0000000000000972
Abstract: Pleuropulmonary blastoma (PPB) is a rare malignancy of childhood which when left untreated often shows pathologic progression resulting in a more aggressive neoplasm with an increasingly poor prognosis. Because of this it is important to… read more here.
Keywords: single center; pleuropulmonary blastoma; treatment; center case ... See more keywords
Pleuropulmonary blastoma type I presenting as a tension pneumothorax: a case report and review of the literature
Sign Up to like & getrecommendations! Published in 2023 at "Annals of Medicine and Surgery"
DOI: 10.1097/ms9.0000000000000514
Abstract: Pleuropulmonary blastoma (PPB) is a very rare, aggressive, embryonal pulmonary malignancy that mostly affects children under the age of 5 years. According to the histological features, three subtypes of PPB have been recognized: type I… read more here.
Keywords: pneumothorax; case; ppb; type ... See more keywords
Pleuropulmonary blastoma in a 3-year-old child with persistent fever: a case report
Sign Up to like & getrecommendations! Published in 2025 at "Frontiers in Pediatrics"
DOI: 10.3389/fped.2025.1534277
Abstract: Pleuropulmonary blastoma (PPB) is a rare and highly aggressive malignant mesenchymal tumor, representing the most common malignant lung tumor in children. It is often misdiagnosed or underdiagnosed due to its clinical presentation, which mimics acute… read more here.
Keywords: pleuropulmonary blastoma; child persistent; blastoma year; year old ... See more keywords
Pleuropulmonary Blastoma in Children: A Nationwide Multicenter Study
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DOI: 10.3390/cancers17193223
Abstract: Simple Summary The aim of the study was to analyze the treatment of pleuropulmonary blastoma (PPB) in a group of 15 pediatric patients, with a median age of 39 months. PPB is a primary, malignant… read more here.
Keywords: pleuropulmonary blastoma; nationwide multicenter; children nationwide; blastoma children ... See more keywords
Exceptional response to radiotherapy in unresectable pleuropulmonary blastoma of a child
Sign Up to like & getrecommendations! Published in 2020 at "Radiation Oncology Journal"
DOI: 10.3857/roj.2020.00290
Abstract: Pleuropulmonary blastoma (PPB) is a rare intrathoracic neoplasm in children. Although surgery with or without chemotherapy mainly conducted, the response of radiotherapy (RT) has not been evaluated yet. For unresectable tumor, RT might be considered… read more here.
Keywords: response radiotherapy; pleuropulmonary blastoma; ppb;
Predictive Factors of Mortality in Pediatric Pleuropulmonary Blastoma: A Surveillance Epidemiology and End Results Database Analysis
Sign Up to like & getrecommendations! Published in 2024 at "Journal of Indian Association of Pediatric Surgeons"
DOI: 10.4103/jiaps.jiaps_235_23
Abstract: ABSTRACT Purpose: Pleuropulmonary blastoma (PPB) is a rare malignancy associated with mutations in the DICER1 gene. Early-stage disease (PPB type I) mimics cystic lung malformations and develops in infants read more here.
Keywords: epidemiology; pleuropulmonary blastoma; ppb; analysis ... See more keywords