Estrogen‐Containing Oral Contraceptives Are Associated With Polycystic Liver Disease Severity in Premenopausal Patients
Sign Up to like & getrecommendations! Published in 2019 at "Clinical Pharmacology and Therapeutics"
DOI: 10.1002/cpt.1553
Abstract: The association between estrogen‐containing oral contraceptives and history of pregnancies with disease severity in women with polycystic liver disease (PLD) is unclear. We performed a cross‐sectional cohort study to assess this association by selecting female… read more here.
Keywords: containing oral; polycystic liver; estrogen containing; disease severity ... See more keywords
En bloc excision of giant polycystic liver with hepatic cava and its auto‐transplant caval reconstruction as a safe surgical procedure for liver transplantation
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Hepato-Biliary-Pancreatic Sciences"
DOI: 10.1002/jhbp.1138
Abstract: Safely excising a giant liver while leaving the hepatic inferior vena cava intact is difficult. Hata et al. present images and videos describing their novel technique consisting of total hepatectomy including the hepatic cava; extracorporeal… read more here.
Keywords: hepatic cava; auto transplant; polycystic liver; liver ... See more keywords
Renal dysfunction after liver transplantation for polycystic liver disease
Sign Up to like & getrecommendations! Published in 2022 at "Liver Transplantation"
DOI: 10.1002/lt.26516
Abstract: To the editor, Polycystic liver disease (PLD) encompasses a group of liver disorders with varying renal involvement.[1] There are no curative treatment options and patients can require liver transplantation (LT), as either isolated LT or… read more here.
Keywords: polycystic liver; liver; transplantation; liver disease ... See more keywords
Targeting UBC9-mediated protein hyper-SUMOylation in cystic cholangiocytes halts polycystic liver disease in experimental models
Sign Up to like & getrecommendations! Published in 2020 at "Journal of hepatology"
DOI: 10.1016/j.jhep.2020.09.010
Abstract: Background & Aims: Polycystic liver diseases (PLDs) are genetic disorders characterized by progressive development of multiple fluid-filled biliary cysts. Most PLD-causative genes participate in protein biogenesis and/or transport. Post-translational modifications (PTMs) are implicated in protein… read more here.
Keywords: sumoylation; protein; polycystic liver; targeting ubc9 ... See more keywords
Trans sigmoid colon NOTES sclerotherapy for polycystic liver disease
Sign Up to like & getrecommendations! Published in 2022 at "Endoscopy"
DOI: 10.1055/a-1887-5737
Abstract: Laparoscopic cystic fluid aspiration is one of the common treatments for polycystic liver disease (PLD) [1]. However, laparoscopes have limited flexibility, and parts of the abdominal cavity are difficult to reach [2]. To avoid the… read more here.
Keywords: polycystic liver; liver; notes sclerotherapy; sclerotherapy polycystic ... See more keywords
Treatment of Polycystic Liver Disease
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Clinical Gastroenterology"
DOI: 10.1097/mcg.0000000000001749
Abstract: Polycystic liver disease (PLD) is a genetic disorder in which patients suffer from progressive development of multiple (>10) hepatic cysts. Most patients remain asymptomatic during the course of their disease. However, a minority of PLD… read more here.
Keywords: polycystic liver; disease; pld; treatment ... See more keywords
Bile Acids in Polycystic Liver Diseases: Triggers of Disease Progression and Potential Solution for Treatment
Sign Up to like & getrecommendations! Published in 2017 at "Digestive Diseases"
DOI: 10.1159/000450989
Abstract: Polycystic liver diseases (PLDs) are a group of genetic hereditary cholangiopathies characterized by the development and progressive growth of cysts in the liver, which are the main cause of morbidity. Current therapies are based on… read more here.
Keywords: bile acids; polycystic liver; liver diseases; treatment ... See more keywords
Isolated polycystic liver disease genes define effectors of polycystin-1 function
Sign Up to like & getrecommendations! Published in 2017 at "Journal of Clinical Investigation"
DOI: 10.1172/jci90129
Abstract: Dominantly inherited isolated polycystic liver disease (PCLD) consists of liver cysts that are radiologically and pathologically identical to those seen in autosomal dominant polycystic kidney disease, but without clinically relevant kidney cysts. The causative genes… read more here.
Keywords: isolated polycystic; polycystic liver; disease; polycystin function ... See more keywords
Liver transplantation in adult polycystic liver disease: the Ontario experience
Sign Up to like & getrecommendations! Published in 2021 at "BMC Gastroenterology"
DOI: 10.1186/s12876-021-01703-x
Abstract: Background Liver transplantation (LT) remains the curative treatment for symptomatic Polycystic Liver Disease (PCLD) patients and is associated with excellent survival rates. The aim of the study is to review the Ontario experience in LT… read more here.
Keywords: ontario experience; polycystic liver; liver; liver transplantation ... See more keywords
Icteric syndrome secondary to polycystic liver disease: Case report.
Sign Up to like & getrecommendations! Published in 2023 at "Revista espanola de enfermedades digestivas"
DOI: 10.17235/reed.2023.9590/2023
Abstract: We present the case of a male patient in the sixth decade of life who attended due to the presence of progressive increase in abdominal circumference, accompanied by early satiety, to which generalized jaundice was… read more here.
Keywords: icteric syndrome; polycystic liver; liver disease; case ... See more keywords
Molecular Mechanisms of Isolated Polycystic Liver Diseases
Sign Up to like & getrecommendations! Published in 2022 at "Frontiers in Genetics"
DOI: 10.3389/fgene.2022.846877
Abstract: Polycystic liver disease (PLD) is a rare autosomal dominant disorder including two genetically and clinically distinct forms: autosomal dominant polycystic kidney disease (ADPKD) and isolated polycystic liver disease (PCLD). The main manifestation of ADPKD is… read more here.
Keywords: polycystic liver; liver; candidate genes; disease ... See more keywords