Articles with "polymorphic ventricular" as a keyword



A 35-year effective treatment of catecholaminergic polymorphic ventricular tachycardia with propafenone

Sign Up to like & get
recommendations!
Published in 2019 at "HeartRhythm Case Reports"

DOI: 10.1016/j.hrcr.2018.04.003

Abstract: Key Teaching Points • Despite proven catecholaminergic polymorphic ventricular tachycardia (CPVT) with pathogen RyR2 mutation and recurrent syncope, patients could have a favorable long-term outcome over 35 years under treatment. • Propafenone could be effective… read more here.

Keywords: ventricular tachycardia; effective treatment; polymorphic ventricular; treatment ... See more keywords
Photo from wikipedia

Scared to death—A novel mutation in catecholaminergic polymorphic ventricular tachycardia

Sign Up to like & get
recommendations!
Published in 2020 at "HeartRhythm Case Reports"

DOI: 10.1016/j.hrcr.2020.01.009

Abstract: The decision to implant an implantable cardioverter-defibrillator in patients with CPVT is challenging, as there are no randomized controlled Introduction Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a rare familial cardiac arrhythmia that results in bidirectional… read more here.

Keywords: death; ventricular tachycardia; polymorphic ventricular; catecholaminergic polymorphic ... See more keywords
Photo from wikipedia

Syncope after successful implantation of atrioventricular synchronous leadless pacemaker caused by polymorphic ventricular tachycardia

Sign Up to like & get
recommendations!
Published in 2020 at "HeartRhythm Case Reports"

DOI: 10.1016/j.hrcr.2020.05.003

Abstract: Introduction Leadless pacing is an alternative to transvenous single-chamber ventricular pacing (VVI/R) with a favorable safety and efficacy profile in selected patients. Until recently, the Micra (Model MC1VR01; Medtronic Inc, Minneapolis, MN) was the only… read more here.

Keywords: ventricular tachycardia; polymorphic ventricular; leadless; implantation ... See more keywords

Hypokalemia unmasking underlying premature ventricular contraction induced polymorphic ventricular tachycardia: Low potassium is not always the culprit!

Sign Up to like & get
recommendations!
Published in 2019 at "Indian Pacing and Electrophysiology Journal"

DOI: 10.1016/j.ipej.2019.12.006

Abstract: Hypokalemia is prevalent in patients resuscitated from out-of-hospital cardiac arrest and can contribute to polymorphic ventricular tachycardia (PMVT) by prolonging the QT interval. We present an interesting scenario of malignant ventricular arrythmia initially attributed to… read more here.

Keywords: potassium; ventricular tachycardia; polymorphic ventricular; hypokalemia unmasking ... See more keywords
Photo by nci from unsplash

SHORT OR LONG: POLYMORPHIC VENTRICULAR TACHYCARDIA ORIGINATING FROM THE PURKINJE SYSTEM

Sign Up to like & get
recommendations!
Published in 2020 at "Journal of the American College of Cardiology"

DOI: 10.1016/s0735-1097(20)33878-x

Abstract: Short coupled variant of Torsades de pointes(TdP) may be responsible for sudden cardiac death in the absence of structural heart disease. Differentiation of this entity from Long QT associated TdP has important therapeutic implications. A… read more here.

Keywords: tachycardia originating; ventricular tachycardia; long polymorphic; polymorphic ventricular ... See more keywords
Photo from wikipedia

Documenting the descent – remote monitoring and adult-onset Catecholaminergic Polymorphic Ventricular Tachycardia associated with ventricular fibrillation and bradycardia

Sign Up to like & get
recommendations!
Published in 2021 at "Cardiology in the Young"

DOI: 10.1017/s1047951121002377

Abstract: Abstract This image highlights a 38-year-old female with ventricular fibrillation and spontaneous return to sinus rhythm found on an implantable loop recorder inserted for recurrent syncope. Ultimately, she was diagnosed with catecholaminergic polymorphic ventricular tachycardia,… read more here.

Keywords: ventricular tachycardia; polymorphic ventricular; catecholaminergic polymorphic; ventricular fibrillation ... See more keywords

Acute in vivo antiarrhythmic effects of cGMP-modifying drugs in the R2474S mouse model of catecholiminergic polymorphic ventricular tachycardia

Sign Up to like & get
recommendations!
Published in 2025 at "Europace"

DOI: 10.1093/europace/euaf085.805

Abstract: Abstract Background Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited arrhythmia syndrome arising from mutations in cardiac calcium regulatory proteins. CPVT has a high mortality rate when left untreated. First-line treatments such as β-blockers have… read more here.

Keywords: polymorphic ventricular; ventricular tachycardia; cgmp modifying; drugs r2474s ... See more keywords
Photo from academic.microsoft.com

Catecholaminergic Polymorphic Ventricular Tachycardia.

Sign Up to like & get
recommendations!
Published in 2017 at "Pediatric emergency care"

DOI: 10.1097/01.pec.0000520710.58614.76

Abstract: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a condition characterized by an abnormal heart rhythm (arrhythmia). As the heart rate increases in response to physical activity or emotional stress, it can trigger an abnormally fast and… read more here.

Keywords: polymorphic ventricular; catecholaminergic polymorphic; ventricular tachycardia; tachycardia ... See more keywords

Unusual catecholaminergic polymorphic ventricular tachycardia and bradycardia caused by a novel triadin variant in 2 siblings from a Malian family

Sign Up to like & get
recommendations!
Published in 2025 at "Medicine"

DOI: 10.1097/md.0000000000043596

Abstract: Rationale: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is a hereditary arrhythmia syndrome that can cause sudden cardiac death, particularly in young individuals. CPVT is often linked to triadin (TRDN) variants that disrupt calcium regulation in the… read more here.

Keywords: polymorphic ventricular; family; ventricular tachycardia; catecholaminergic polymorphic ... See more keywords

A gain of function ryanodine receptor 2 mutation (R1760W‐RyR2) in catecholaminergic polymorphic ventricular tachycardia

Sign Up to like & get
recommendations!
Published in 2022 at "Clinical and Experimental Pharmacology and Physiology"

DOI: 10.1111/1440-1681.13722

Abstract: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited arrhythmia syndrome associated with Ca2+ leak predominantly caused by ryanodine receptor 2 (RyR2) mutations. We identified a R1760W‐RyR2 mutation located between the N‐terminal domain and the central… read more here.

Keywords: polymorphic ventricular; catecholaminergic polymorphic; r1760w ryr2; ryr2 ... See more keywords

Efficacy of RyR2 inhibitor EL20 in induced pluripotent stem cell‐derived cardiomyocytes from a patient with catecholaminergic polymorphic ventricular tachycardia

Sign Up to like & get
recommendations!
Published in 2021 at "Journal of Cellular and Molecular Medicine"

DOI: 10.1111/jcmm.16521

Abstract: Catecholaminergic polymorphic ventricular tachycardia (CPVT) is an inherited cardiac arrhythmia syndrome that often leads to sudden cardiac death. The most common form of CPVT is caused by autosomal‐dominant variants in the cardiac ryanodine receptor type‐2… read more here.

Keywords: el20; ventricular tachycardia; polymorphic ventricular; ryr2 ... See more keywords