Increased mortality in patients with porphyria cutanea tarda - a nationwide cohort study.
Sign Up to like & getrecommendations! Published in 2019 at "Journal of the American Academy of Dermatology"
DOI: 10.1016/j.jaad.2019.07.082
Abstract: BACKGROUND Porphyria cutanea tarda (PCT) is a rare hepatocutaneous disease whose prognosis is largely unknown. OBJECTIVES To compare all-cause and cause-specific mortality between a nationwide cohort of patients with PCT and a matched population sample.… read more here.
Keywords: increased mortality; mortality; porphyria cutanea; nationwide cohort ... See more keywords
Porphyria cutanea tarda unmasked by supratherapeutic estrogen during gender-affirming hormone therapy
Sign Up to like & getrecommendations! Published in 2020 at "JAAD Case Reports"
DOI: 10.1016/j.jdcr.2020.04.036
Abstract: HT: hormone therapy PCT: porphyria cutanea tarda INTRODUCTION Providing medically competent care for gender minorities has become a public health focus. Bodygender incongruence, antitransgender biases, and social isolation contribute to a lifetime risk of suicide… read more here.
Keywords: porphyria cutanea; hormone; hormone therapy; cutanea tarda ... See more keywords
Between a rock and a hard place: management of systemic lupus erythematosus and porphyria cutanea tarda
Sign Up to like & getrecommendations! Published in 2022 at "Journal of Dermatological Treatment"
DOI: 10.1080/09546634.2022.2060925
Abstract: Abstract Porphyria cutanea tarda (PCT), the most common porphyria, is a rare photodermatosis characterized by fragile, hemorrhagic bullae and erosions with associated milia, hyperpigmentation, and hypertrichosis. SLE is a systemic connective tissue disease with approximately… read more here.
Keywords: management; porphyria cutanea; cutanea tarda; porphyria ... See more keywords
Sight-threatening progressive corneo-scleral involvement in porphyria cutanea tarda
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DOI: 10.1136/bcr-2021-245160
Abstract: Porphyria cutanea tarda is the most common type of porphyria. It is associated with a deficiency of uroporphyrinogen decarboxylase enzyme responsible for heme synthesis. Clinical manifestations are predominantly dermatological and very rarely present with ocular… read more here.
Keywords: corneo scleral; porphyria cutanea; sight threatening; involvement ... See more keywords
Case 304: Porphyria Cutanea Tarda.
Sign Up to like & getrecommendations! Published in 2022 at "Radiology"
DOI: 10.1148/radiol.204599
Abstract: HISTORY In 2017, a 72-year-old woman was seen in the gastroenterology department with a 2-month history of mild and intermittent abdominal pain without other accompanying symptoms. Her medical history was unremarkable, except for a previous… read more here.
Keywords: case 304; history; porphyria cutanea; cutanea tarda ... See more keywords
Genetic ancestry of patients with porphyria cutanea tarda in a country with mixed races: a cross-sectional study (Rio de Janeiro - Brazil).
Sign Up to like & getrecommendations! Published in 2018 at "Anais brasileiros de dermatologia"
DOI: 10.1590/abd1806-4841.20186666
Abstract: Porphyria cutanea tarda has a complex etiology with genetic factors not completely elucidated. The miscegenation of the Brazilian population has important implications in the predisposition to diseases. There are no studies concerning the genetic ancestry… read more here.
Keywords: ancestry patients; porphyria cutanea; patients porphyria; genetic ancestry ... See more keywords
What is your diagnosis?: Case for diagnosis. Sclerodermiform manifestations of porphyria cutanea tarda secondary to hepatitis C.
Sign Up to like & getrecommendations! Published in 2019 at "Anais brasileiros de dermatologia"
DOI: 10.1590/abd1806-4841.20198681
Abstract: A 63-year-old black female patient with blisters and exulcerations on the face, neck, upper limbs, and subsequent evolution with hypochromic sclerotic areas and alopecia, is reported. Chronic hepatitis C and presence of high levels of… read more here.
Keywords: secondary hepatitis; diagnosis; hepatitis; porphyria cutanea ... See more keywords
sQuiz your knowledge: Expanding scarring alopecia in a patient with porphyria cutanea tarda
Sign Up to like & getrecommendations! Published in 2017 at "European Journal of Dermatology"
DOI: 10.1684/ejd.2017.3005
Abstract: A 55-year-old male with a history of untreated hepatitis C infection, chronic liver disease, and porphyria cutanea tarda (PCT) was seen for scarring alopecia on the scalp that evolved over a period of a year… read more here.
Keywords: porphyria cutanea; squiz knowledge; scarring alopecia; cutanea tarda ... See more keywords