Clinico-radiologic features of pleuroparenchymal fibroelastosis in children
Sign Up to like & getrecommendations! Published in 2019 at "Pediatric Radiology"
DOI: 10.1007/s00247-019-04405-5
Abstract: BackgroundPleuroparenchymal fibroelastosis (PPFE) may be underdiagnosed clinically and radiographically in children with a remote history of cancer, leading to a delay in care and unnecessary lung biopsies.ObjectiveTo describe the characteristic clinical and radiologic findings of… read more here.
Keywords: radiology; history; ppfe; cancer ... See more keywords
Pediatric Lung Transplant for Pleuroparenchymal Fibroelastosis: Single Center Experience
Sign Up to like & getrecommendations! Published in 2021 at "Journal of Heart and Lung Transplantation"
DOI: 10.1016/j.healun.2021.01.1000
Abstract: Purpose Pleuroparenchymal fibroelastosis (PPFE) is a rare, progressive, restrictive lung disease characterized by hypercarbic respiratory failure. In pediatrics, it has been described in patients with a history of malignancy who have received a bone marrow… read more here.
Keywords: ppfe; lung; transplant; center ... See more keywords
Clinical, radiological, and pathological features of idiopathic and secondary interstitial pneumonia cases with pleuroparenchymal fibroelastosis undergoing lung transplantation.
Sign Up to like & getrecommendations! Published in 2021 at "Histopathology"
DOI: 10.1111/his.14595
Abstract: AIMS Idiopathic pleuroparenchymal fibroelastosis (PPFE) is a rare type of idiopathic interstitial pneumonia, and pathological PPFE is also observed in secondary interstitial pneumonia. This study aimed to evaluate the pathological findings associated with radiological PPFE-like… read more here.
Keywords: pathological ppfe; idiopathic secondary; secondary cases; ppfe ... See more keywords
Prognostic significance of radiological pleuroparenchymal fibroelastosis in Mycobacterium avium complex lung disease: a multicentre retrospective cohort study
Sign Up to like & getrecommendations! Published in 2022 at "Thorax"
DOI: 10.1136/thorax-2022-219116
Abstract: Background Mycobacterium avium complex (MAC) causes chronic respiratory infectious diseases with diverse clinical features and prognoses. Pleuroparenchymal fibroelastosis (PPFE) is a rare disease characterised by pleural fibrosis with subjacent intra-alveolar fibrosis and alveolar septal elastosis,… read more here.
Keywords: ppfe; study; radiological ppfe; lung disease ... See more keywords
Delineating associations of progressive pleuroparenchymal fibroelastosis in patients with pulmonary fibrosis
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DOI: 10.1183/23120541.00637-2022
Abstract: Background Computer quantification of baseline computed tomography (CT) radiological pleuroparenchymal fibroelastosis (PPFE) associates with mortality in idiopathic pulmonary fibrosis (IPF). We examined mortality associations of longitudinal change in computer-quantified PPFE-like lesions in IPF and fibrotic… read more here.
Keywords: ppfe; ppfe like; like lesions; pleuroparenchymal fibroelastosis ... See more keywords
Unilateral pleuroparenchymal fibroelastosis as a rare form of idiopathic interstitial pneumonia: A case report
Sign Up to like & getrecommendations! Published in 2020 at "World Journal of Clinical Cases"
DOI: 10.12998/wjcc.v8.i18.4186
Abstract: BACKGROUND Pleuroparenchymal fibroelastosis (PPFE) is a rare idiopathic interstitial pneumonia characterized by predominantly upper lobe involvement with pleural fibrosis and subjacent parenchymal fibrosis. Recently, there have been increasing reports of PPFE, and PPFE might coexist… read more here.
Keywords: pleuroparenchymal fibroelastosis; idiopathic interstitial; lobe; ppfe ... See more keywords
Pleuroparenchymal Fibroelastosis-like Lesions in Clinical Practice: A Rare Entity? Review of a Radiological Database
Sign Up to like & getrecommendations! Published in 2023 at "Diagnostics"
DOI: 10.3390/diagnostics13091627
Abstract: Background: Pleuroparenchymal Fibroelastosis (PPFE) is a rare disease that consists of elastofibrosis that involves the pleura and subpleural lung parenchyma; it is an unusual pulmonary disease with unique clinical, radiological and pathological characteristics. According to… read more here.
Keywords: ppfe; disease; like lesions; pleuroparenchymal fibroelastosis ... See more keywords