Mimics of Pediatric Small Vessel Primary Angiitis of the Central Nervous System
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DOI: 10.1002/ana.26531
Abstract: Small vessel primary angiitis of the central nervous system is a rare and often severe disease characterized by central nervous system‐restricted inflammatory vasculitis on histopathology. Diagnosis requires brain biopsy for confirmation and is suggested prior… read more here.
Keywords: vessel primary; central nervous; small vessel; primary angiitis ... See more keywords
Cortical Microhemorrhage Presentation of Small Vessel Primary Angiitis of the Central Nervous System
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DOI: 10.1002/ana.26940
Abstract: Primary angiitis of the central nervous system (PACNS) is a rare vasculitis restricted to the brain, spinal cord, and leptomeninges. This study aimed to describe the imaging characteristics of patients with small vessel PACNS (SV‐PACNS)… read more here.
Keywords: small vessel; central nervous; nervous system; angiitis central ... See more keywords
Diagnostic MRI Score to Differentiate Susac Syndrome from Primary Angiitis of the Central Nervous System and Multiple Sclerosis
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DOI: 10.1002/ana.27043
Abstract: Susac syndrome (SuS), multiple sclerosis (MS), and primary angiitis of the central nervous system (PACNS) present diagnostic challenges due to overlapping clinical features. We aimed to enhance diagnostic precision by developing the SPAMS (SuS, PACNS,… read more here.
Keywords: central nervous; multiple sclerosis; nervous system; susac syndrome ... See more keywords
An ischemic stroke as the presenting manifestation of rapidly progressive primary angiitis of central nervous system in a 17-year-old boy
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DOI: 10.1016/j.jneuroim.2020.577190
Abstract: BACKGROUND Childhood primary angiitis of the central nervous system (cPACNS) is an increasingly recognized inflammatory brain disease in children. CASE PRESENTATION We present a case of a 17-year-old boy with recurrent ischemic events over a… read more here.
Keywords: primary angiitis; angiitis central; nervous system; central nervous ... See more keywords
Primary angiitis of the central nervous system mimicking a cerebellar tumor
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DOI: 10.1080/02688697.2018.1464122
Abstract: Abstract Primary angiitis of the central nervous system (PACNS), is a rare and poorly understood disease mainly characterized by multifocal segmental inflammation of the small and medium vessels of the central nervous system. Most PACNS… read more here.
Keywords: primary angiitis; nervous system; central nervous; cerebellar tumor ... See more keywords
Close, but no cigar: an unfortunate case of primary angiitis of the central nervous system
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DOI: 10.1097/ms9.0000000000000084
Abstract: Introduction: Primary angiitis of the central nervous system (PACNS) is an uncommon and misunderstood disease, where little is known regarding its immunopathogenesis and appropriate treatment. Due to the constellation of nonspecific clinical features and imaging… read more here.
Keywords: central nervous; primary angiitis; case; angiitis central ... See more keywords
Differentiating primary angiitis of the central nervous system from paraneoplastic neurological syndrome
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DOI: 10.1136/bcr-2025-266850
Abstract: Primary angiitis of the central nervous system (PACNS) is a rare, inflammatory condition affecting small- and medium-sized vessels in the brain and spinal cord. Its diagnosis presents challenges due to nonspecific symptoms that mimic various… read more here.
Keywords: central nervous; nervous system; angiitis central; primary angiitis ... See more keywords
Application of High-Resolution Magnetic Resonance Vessel Wall Imaging in Childhood Primary Angiitis of the Central Nervous System.
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DOI: 10.1177/08830738251348795
Abstract: Background Childhood primary angiitis of the central nervous system is a rare inflammatory disorder affecting the central nervous system in children. High-resolution magnetic resonance vessel wall imaging is less frequently used in the childhood primary… read more here.
Keywords: central nervous; primary angiitis; nervous system; vessel wall ... See more keywords
Primary angiitis of the central nervous system: diagnosis and treatment
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DOI: 10.1177/1756286418785071
Abstract: Primary angiitis of the central nervous system (PACNS) represents a rare inflammatory disease affecting the brain and spinal cord. Stroke, encephalopathy, headache and seizures are major clinical manifestations. The diagnosis of PACNS is based on… read more here.
Keywords: primary angiitis; angiitis central; diagnosis; nervous system ... See more keywords
Temporal evolution of primary angiitis of the central nervous system (PACNS) on MRI following immunosuppressant treatment
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DOI: 10.1186/s13244-024-01710-y
Abstract: To systematically analyse the time course of vessel wall enhancement and associated stenosis in patients with primary angiitis of the central nervous system (PACNS) following immunosuppressive therapy. Two neuroradiologists retrospectively analysed MRIs of patients with… read more here.
Keywords: wall enhancement; primary angiitis; vessel wall;
Size of affected vessels in primary angiitis of the CNS: associations with clinical features, medical management and functional outcomes
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DOI: 10.3389/fneur.2025.1613701
Abstract: Background Primary angiitis of the central nervous system (PACNS) presents with heterogeneous clinical manifestations. Since implications of specific patterns of vessel size involvement are not well elucidated, this study aimed to investigate individual disease courses… read more here.
Keywords: small vessel; size; vessel involvement; primary angiitis ... See more keywords